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Scientific Reports
|
July 14, 2017
Inhibition of β-Glucocerebrosidase Activity Preserves Motor Unit Integrity in a Mouse Model of Amyotrophic Lateral Sclerosis
Alexandre Henriques, Mylene Huebecker, Hélène Blasco, et al.
Analytical Biochemistry
|
July 22, 2004
Analysis of fluorescently labeled glycosphingolipid-derived oligosaccharides following ceramide glycanase digestion and anthranilic acid labeling
David C A Neville, Virginie Coquard, David A Priestman, et al.
Iscience
|
September 1, 2021
A modified density gradient proteomic-based method to analyze endolysosomal proteins in cardiac tissue
Thamali Ayagama, Samuel J Bose, Rebecca A Capel, et al.
International Journal of Molecular Sciences
|
March 11, 2023
A Mouse Systems Genetics Approach Reveals Common and Uncommon Genetic Modifiers of Hepatic Lysosomal Enzyme Activities and Glycosphingolipids
Anyelo Durán, David A Priestman, Macarena Las Heras, et al.
Biochemistry and Biophysics Reports
|
August 30, 2021
Identification of genetic modifiers of murine hepatic β-glucocerebrosidase activity
Anyelo Durán, Boris Rebolledo-Jaramillo, Valeria Olguin, et al.
Journal of Medicinal Chemistry
|
November 8, 2017
N-Butyl-l-deoxynojirimycin (l-NBDNJ): Synthesis of an Allosteric Enhancer of α-Glucosidase Activity for the Treatment of Pompe Disease
Daniele D'Alonzo, Maria De Fenza, Caterina Porto, et al.
Acta Neuropathologica Communications
|
August 9, 2020
Upregulating β-hexosaminidase activity in rodents prevents α-synuclein lipid associations and protects dopaminergic neurons from α-synuclein-mediated neurotoxicity
Oeystein R Brekk, Joanna A Korecka, Cecile C Crapart, et al.
Plos Biology
|
July 3, 2025
Plasma membrane remodeling in GM2 gangliosidoses drives synaptic dysfunction
Alex S Nicholson, David A Priestman, Robin Antrobus, et al.
Proceedings of the National Academy of Sciences of the United States of America
|
March 21, 2007
Implications for invariant natural killer T cell ligands due to the restricted presence of isoglobotrihexosylceramide in mammals
Anneliese O Speak, Mariolina Salio, David C A Neville, et al.
The Journal of Experimental Medicine
|
June 15, 2022
Glucosamine amends CNS pathology in mucopolysaccharidosis IIIC mouse expressing misfolded HGSNAT
Xuefang Pan, Mahsa Taherzadeh, Poulomee Bose, et al.
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Search research articles
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Showing results (11-20 of 34) with videos related to
Sort By:
Page
of 4
Scientific Reports
|
July 14, 2017
Inhibition of β-Glucocerebrosidase Activity Preserves Motor Unit Integrity in a Mouse Model of Amyotrophic Lateral Sclerosis
Alexandre Henriques, Mylene Huebecker, Hélène Blasco, et al.
Analytical Biochemistry
|
July 22, 2004
Analysis of fluorescently labeled glycosphingolipid-derived oligosaccharides following ceramide glycanase digestion and anthranilic acid labeling
David C A Neville, Virginie Coquard, David A Priestman, et al.
Iscience
|
September 1, 2021
A modified density gradient proteomic-based method to analyze endolysosomal proteins in cardiac tissue
Thamali Ayagama, Samuel J Bose, Rebecca A Capel, et al.
International Journal of Molecular Sciences
|
March 11, 2023
A Mouse Systems Genetics Approach Reveals Common and Uncommon Genetic Modifiers of Hepatic Lysosomal Enzyme Activities and Glycosphingolipids
Anyelo Durán, David A Priestman, Macarena Las Heras, et al.
Biochemistry and Biophysics Reports
|
August 30, 2021
Identification of genetic modifiers of murine hepatic β-glucocerebrosidase activity
Anyelo Durán, Boris Rebolledo-Jaramillo, Valeria Olguin, et al.
Journal of Medicinal Chemistry
|
November 8, 2017
N-Butyl-l-deoxynojirimycin (l-NBDNJ): Synthesis of an Allosteric Enhancer of α-Glucosidase Activity for the Treatment of Pompe Disease
Daniele D'Alonzo, Maria De Fenza, Caterina Porto, et al.
Acta Neuropathologica Communications
|
August 9, 2020
Upregulating β-hexosaminidase activity in rodents prevents α-synuclein lipid associations and protects dopaminergic neurons from α-synuclein-mediated neurotoxicity
Oeystein R Brekk, Joanna A Korecka, Cecile C Crapart, et al.
Plos Biology
|
July 3, 2025
Plasma membrane remodeling in GM2 gangliosidoses drives synaptic dysfunction
Alex S Nicholson, David A Priestman, Robin Antrobus, et al.
Proceedings of the National Academy of Sciences of the United States of America
|
March 21, 2007
Implications for invariant natural killer T cell ligands due to the restricted presence of isoglobotrihexosylceramide in mammals
Anneliese O Speak, Mariolina Salio, David C A Neville, et al.
The Journal of Experimental Medicine
|
June 15, 2022
Glucosamine amends CNS pathology in mucopolysaccharidosis IIIC mouse expressing misfolded HGSNAT
Xuefang Pan, Mahsa Taherzadeh, Poulomee Bose, et al.
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of 4