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Derek Burke

Showing results (31-40 of 43) with videos related to

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Neurology|October 10, 2014
Cathepsin D deficiency causes juvenile-onset ataxia and distinctive muscle pathologyJoshua Hersheson, Derek Burke, Robert Clayton, et al.
Molecular Therapy. Methods & Clinical Development|October 27, 2021
Safety and efficacy of an engineered hepatotropic AAV gene therapy for ornithine transcarbamylase deficiency in cynomolgus monkeysJulien Baruteau, Sharon C Cunningham, Berna Seker Yilmaz, et al.
Movement Disorders : Official Journal of the Movement Disorder Society|February 13, 2013
Movement disorders in adult patients with classical galactosemiaIgnacio Rubio-Agusti, Miryam Carecchio, Kailash P Bhatia, et al.
Analytical Chemistry|November 6, 2015
Proteomic Discovery and Development of a Multiplexed Targeted MRM-LC-MS/MS Assay for Urine Biomarkers of Extracellular Matrix Disruption in Mucopolysaccharidoses I, II, and VIWendy E Heywood, Stephane Camuzeaux, Ivan Doykov, et al.
Molecular Therapy. Methods & Clinical Development|August 11, 2020
Lentiviral Hematopoietic Stem Cell Gene Therapy Rescues Clinical Phenotypes in a Murine Model of Pompe DiseaseGiuseppa Piras, Claudia Montiel-Equihua, Yee-Ka Agnes Chan, et al.
American Journal of Medical Genetics. Part C, Seminars in Medical Genetics|August 10, 2020
A genetic and clinical study of individuals with nonsyndromic retinopathy consequent upon sequence variants in HGSNAT, the gene associated with Sanfilippo C mucopolysaccharidosisElena R Schiff, Malena Daich Varela, Anthony G Robson, et al.
Molecular Genetics and Metabolism|August 25, 2016
Diagnosis of neuronal ceroid lipofuscinosis type 2 (CLN2 disease): Expert recommendations for early detection and laboratory diagnosisMichael Fietz, Moeenaldeen AlSayed, Derek Burke, et al.
Analytical Chemistry|August 8, 2017
An LC-MS/MS-Based Method for the Quantification of Pyridox(am)ine 5'-Phosphate Oxidase Activity in Dried Blood Spots from Patients with EpilepsyMatthew P Wilson, Emma J Footitt, Apostolos Papandreou, et al.
Human Molecular Genetics|September 18, 2015
Glucocerebrosidase 1 deficient Danio rerio mirror key pathological aspects of human Gaucher disease and provide evidence of early microglial activation preceding alpha-synuclein-independent neuronal cell deathMarcus Keatinge, Hai Bui, Aswin Menke, et al.
Nature Medicine|July 18, 2018
Fetal gene therapy for neurodegenerative disease of infantsGiulia Massaro, Citra N Z Mattar, Andrew M S Wong, et al.
Pageof 5

Showing results (31-40 of 43) with videos related to

Sort By:
Pageof 5
Neurology|October 10, 2014
Cathepsin D deficiency causes juvenile-onset ataxia and distinctive muscle pathologyJoshua Hersheson, Derek Burke, Robert Clayton, et al.
Molecular Therapy. Methods & Clinical Development|October 27, 2021
Safety and efficacy of an engineered hepatotropic AAV gene therapy for ornithine transcarbamylase deficiency in cynomolgus monkeysJulien Baruteau, Sharon C Cunningham, Berna Seker Yilmaz, et al.
Movement Disorders : Official Journal of the Movement Disorder Society|February 13, 2013
Movement disorders in adult patients with classical galactosemiaIgnacio Rubio-Agusti, Miryam Carecchio, Kailash P Bhatia, et al.
Analytical Chemistry|November 6, 2015
Proteomic Discovery and Development of a Multiplexed Targeted MRM-LC-MS/MS Assay for Urine Biomarkers of Extracellular Matrix Disruption in Mucopolysaccharidoses I, II, and VIWendy E Heywood, Stephane Camuzeaux, Ivan Doykov, et al.
Molecular Therapy. Methods & Clinical Development|August 11, 2020
Lentiviral Hematopoietic Stem Cell Gene Therapy Rescues Clinical Phenotypes in a Murine Model of Pompe DiseaseGiuseppa Piras, Claudia Montiel-Equihua, Yee-Ka Agnes Chan, et al.
American Journal of Medical Genetics. Part C, Seminars in Medical Genetics|August 10, 2020
A genetic and clinical study of individuals with nonsyndromic retinopathy consequent upon sequence variants in HGSNAT, the gene associated with Sanfilippo C mucopolysaccharidosisElena R Schiff, Malena Daich Varela, Anthony G Robson, et al.
Molecular Genetics and Metabolism|August 25, 2016
Diagnosis of neuronal ceroid lipofuscinosis type 2 (CLN2 disease): Expert recommendations for early detection and laboratory diagnosisMichael Fietz, Moeenaldeen AlSayed, Derek Burke, et al.
Analytical Chemistry|August 8, 2017
An LC-MS/MS-Based Method for the Quantification of Pyridox(am)ine 5'-Phosphate Oxidase Activity in Dried Blood Spots from Patients with EpilepsyMatthew P Wilson, Emma J Footitt, Apostolos Papandreou, et al.
Human Molecular Genetics|September 18, 2015
Glucocerebrosidase 1 deficient Danio rerio mirror key pathological aspects of human Gaucher disease and provide evidence of early microglial activation preceding alpha-synuclein-independent neuronal cell deathMarcus Keatinge, Hai Bui, Aswin Menke, et al.
Nature Medicine|July 18, 2018
Fetal gene therapy for neurodegenerative disease of infantsGiulia Massaro, Citra N Z Mattar, Andrew M S Wong, et al.
Pageof 5