Jove
Visualize
Contact Us
JoVE
x logofacebook logolinkedin logoyoutube logo
ABOUT JoVE
OverviewLeadershipBlogJoVE Help Center
AUTHORS
Publishing ProcessEditorial BoardScope & PoliciesPeer ReviewFAQSubmit
LIBRARIANS
TestimonialsSubscriptionsAccessResourcesLibrary Advisory BoardFAQ
RESEARCH
JoVE JournalMethods CollectionsJoVE Encyclopedia of ExperimentsArchive
EDUCATION
JoVE CoreJoVE BusinessJoVE Science EducationJoVE Lab ManualFaculty Resource CenterFaculty Site
Terms & Conditions of Use
Privacy Policy
Policies

Filters

Dirk Lefeber

Showing results (61-70 of 72) with videos related to

Pageof 8
Sort By:
Frontiers in Immunology|September 8, 2025
Glycoproteomics analysis of complement factor H and its complement-regulatory function during <i>Streptococcus pneumoniae</i>-associated hemolytic uremic syndromeLaura M Baas, Kioa L Wijnsma, Fokje Zijlstra, et al.
Nature Genetics|December 25, 2007
Impaired glycosylation and cutis laxa caused by mutations in the vesicular H+-ATPase subunit ATP6V0A2Uwe Kornak, Ellen Reynders, Aikaterini Dimopoulou, et al.
Nature Communications|October 29, 2021
Congenital disorder of glycosylation caused by starting site-specific variant in syntaxin-5Peter T A Linders, Eveline C F Gerretsen, Angel Ashikov, et al.
European Journal of Human Genetics : EJHG|August 22, 2013
Clinical and biochemical features guiding the diagnostics in neurometabolic cutis laxaThatjana Gardeitchik, Miski Mohamed, Björn Fischer, et al.
The Journal of Clinical Endocrinology and Metabolism|October 15, 2010
Autosomal recessive mental retardation, deafness, ankylosis, and mild hypophosphatemia associated with a novel ANKH mutation in a consanguineous familyEva Morava, Jirko Kühnisch, Jefte M Drijvers, et al.
Journal of Inherited Metabolic Disease|December 5, 2024
Clinical severity and cardiac phenotype in phosphomannomutase 2-congenital disorders of glycosylation : Insights into genetics and management recommendationsVeronika Holubova, Rita Barone, Stephanie Grunewald, et al.
The Journal of Pediatrics|May 22, 2016
Defining the Phenotype and Assessing Severity in Phosphoglucomutase-1 DeficiencySunnie Yan-Wai Wong, Lesa J Beamer, Therese Gadomski, et al.
Human Mutation|September 15, 2017
Biallelic variants in WARS2 encoding mitochondrial tryptophanyl-tRNA synthase in six individuals with mitochondrial encephalopathySaskia B Wortmann, Sharita Timal, Hanka Venselaar, et al.
Journal of Inherited Metabolic Disease|May 4, 2022
How to proceed after "negative" exome: A review on genetic diagnostics, limitations, challenges, and emerging new multiomics techniquesSaskia B Wortmann, Machteld M Oud, Mariëlle Alders, et al.
Journal of Inherited Metabolic Disease|July 19, 2020
International consensus guidelines for phosphoglucomutase 1 deficiency (PGM1-CDG): Diagnosis, follow-up, and managementRuqaiah Altassan, Silvia Radenkovic, Andrew C Edmondson, et al.
Pageof 8

Showing results (61-70 of 72) with videos related to

Sort By:
Pageof 8
Frontiers in Immunology|September 8, 2025
Glycoproteomics analysis of complement factor H and its complement-regulatory function during <i>Streptococcus pneumoniae</i>-associated hemolytic uremic syndromeLaura M Baas, Kioa L Wijnsma, Fokje Zijlstra, et al.
Nature Genetics|December 25, 2007
Impaired glycosylation and cutis laxa caused by mutations in the vesicular H+-ATPase subunit ATP6V0A2Uwe Kornak, Ellen Reynders, Aikaterini Dimopoulou, et al.
Nature Communications|October 29, 2021
Congenital disorder of glycosylation caused by starting site-specific variant in syntaxin-5Peter T A Linders, Eveline C F Gerretsen, Angel Ashikov, et al.
European Journal of Human Genetics : EJHG|August 22, 2013
Clinical and biochemical features guiding the diagnostics in neurometabolic cutis laxaThatjana Gardeitchik, Miski Mohamed, Björn Fischer, et al.
The Journal of Clinical Endocrinology and Metabolism|October 15, 2010
Autosomal recessive mental retardation, deafness, ankylosis, and mild hypophosphatemia associated with a novel ANKH mutation in a consanguineous familyEva Morava, Jirko Kühnisch, Jefte M Drijvers, et al.
Journal of Inherited Metabolic Disease|December 5, 2024
Clinical severity and cardiac phenotype in phosphomannomutase 2-congenital disorders of glycosylation : Insights into genetics and management recommendationsVeronika Holubova, Rita Barone, Stephanie Grunewald, et al.
The Journal of Pediatrics|May 22, 2016
Defining the Phenotype and Assessing Severity in Phosphoglucomutase-1 DeficiencySunnie Yan-Wai Wong, Lesa J Beamer, Therese Gadomski, et al.
Human Mutation|September 15, 2017
Biallelic variants in WARS2 encoding mitochondrial tryptophanyl-tRNA synthase in six individuals with mitochondrial encephalopathySaskia B Wortmann, Sharita Timal, Hanka Venselaar, et al.
Journal of Inherited Metabolic Disease|May 4, 2022
How to proceed after "negative" exome: A review on genetic diagnostics, limitations, challenges, and emerging new multiomics techniquesSaskia B Wortmann, Machteld M Oud, Mariëlle Alders, et al.
Journal of Inherited Metabolic Disease|July 19, 2020
International consensus guidelines for phosphoglucomutase 1 deficiency (PGM1-CDG): Diagnosis, follow-up, and managementRuqaiah Altassan, Silvia Radenkovic, Andrew C Edmondson, et al.
Pageof 8