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Don Mahuran

Showing results (1-10 of 19) with videos related to

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Molecular Genetics and Metabolism|January 27, 2009
Diltiazem, a L-type Ca(2+) channel blocker, also acts as a pharmacological chaperone in Gaucher patient cellsBrigitte Rigat, Don Mahuran
Molecular Therapy : the Journal of the American Society of Gene Therapy|December 15, 2020
Letter to the EditorBrian L Mark, Don Mahuran
The FEBS Journal|September 27, 2007
Lending a helping hand, screening chemical libraries for compounds that enhance beta-hexosaminidase A activity in GM2 gangliosidosis cellsMichael B Tropak, Don Mahuran
Biochemical and Biophysical Research Communications|June 3, 2009
GM2 activator protein inhibits platelet activating factor signaling in ratsBrigitte Rigat, Herman Yeger, Darakhshanda Shehnaz, et al.
Biochimica Et Biophysica Acta|January 16, 2003
A single site in human beta-hexosaminidase A binds both 6-sulfate-groups on hexosamines and the sialic acid moiety of GM2 gangliosideRohita Sharma, Scott Bukovac, John Callahan, et al.
Biochemical and Biophysical Research Communications|October 16, 2004
An alpha-subunit loop structure is required for GM2 activator protein binding by beta-hexosaminidase AMaryam Zarghooni, Scott Bukovac, Michael Tropak, et al.
Chembiochem : a European Journal of Chemical Biology|July 14, 2011
Synthesis, kinetic evaluation and cell-based analysis of C-alkylated isofagomines as chaperones of β-glucocerebrosidaseTara Hill, Michael B Tropak, Don Mahuran, et al.
Plos One|September 30, 2011
Characterization of the biosynthesis, processing and kinetic mechanism of action of the enzyme deficient in mucopolysaccharidosis IIICXiaolian Fan, Ilona Tkachyova, Ankit Sinha, et al.
The Journal of Biological Chemistry|January 16, 2004
Pharmacological enhancement of beta-hexosaminidase activity in fibroblasts from adult Tay-Sachs and Sandhoff PatientsMichael B Tropak, Stephen P Reid, Marianne Guiral, et al.
Chemistry & Biology|February 24, 2007
High-throughput screening for human lysosomal beta-N-Acetyl hexosaminidase inhibitors acting as pharmacological chaperonesMichael B Tropak, Jan E Blanchard, Stephen G Withers, et al.
Pageof 2

Showing results (1-10 of 19) with videos related to

Sort By:
Pageof 2
Molecular Genetics and Metabolism|January 27, 2009
Diltiazem, a L-type Ca(2+) channel blocker, also acts as a pharmacological chaperone in Gaucher patient cellsBrigitte Rigat, Don Mahuran
Molecular Therapy : the Journal of the American Society of Gene Therapy|December 15, 2020
Letter to the EditorBrian L Mark, Don Mahuran
The FEBS Journal|September 27, 2007
Lending a helping hand, screening chemical libraries for compounds that enhance beta-hexosaminidase A activity in GM2 gangliosidosis cellsMichael B Tropak, Don Mahuran
Biochemical and Biophysical Research Communications|June 3, 2009
GM2 activator protein inhibits platelet activating factor signaling in ratsBrigitte Rigat, Herman Yeger, Darakhshanda Shehnaz, et al.
Biochimica Et Biophysica Acta|January 16, 2003
A single site in human beta-hexosaminidase A binds both 6-sulfate-groups on hexosamines and the sialic acid moiety of GM2 gangliosideRohita Sharma, Scott Bukovac, John Callahan, et al.
Biochemical and Biophysical Research Communications|October 16, 2004
An alpha-subunit loop structure is required for GM2 activator protein binding by beta-hexosaminidase AMaryam Zarghooni, Scott Bukovac, Michael Tropak, et al.
Chembiochem : a European Journal of Chemical Biology|July 14, 2011
Synthesis, kinetic evaluation and cell-based analysis of C-alkylated isofagomines as chaperones of β-glucocerebrosidaseTara Hill, Michael B Tropak, Don Mahuran, et al.
Plos One|September 30, 2011
Characterization of the biosynthesis, processing and kinetic mechanism of action of the enzyme deficient in mucopolysaccharidosis IIICXiaolian Fan, Ilona Tkachyova, Ankit Sinha, et al.
The Journal of Biological Chemistry|January 16, 2004
Pharmacological enhancement of beta-hexosaminidase activity in fibroblasts from adult Tay-Sachs and Sandhoff PatientsMichael B Tropak, Stephen P Reid, Marianne Guiral, et al.
Chemistry & Biology|February 24, 2007
High-throughput screening for human lysosomal beta-N-Acetyl hexosaminidase inhibitors acting as pharmacological chaperonesMichael B Tropak, Jan E Blanchard, Stephen G Withers, et al.
Pageof 2