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Clinica Chimica Acta; International Journal of Clinical Chemistry|December 22, 1980
Assay of ganglioside GM2-N-acetyl-beta-D-galactosaminidase activity in human fibroblasts employing the natural activator protein--diagnosis of variant forms of GM2 gangliosidosisA Erzberger, E Conzelmann, K Sandhoff
The Journal of Biological Chemistry|October 25, 1983
Activator protein for the degradation of globotriaosylceramide by human alpha-galactosidaseS Gärtner, E Conzelmann, K Sandhoff
Human Genetics|March 1, 1992
Quantitative correlation between the residual activity of beta-hexosaminidase A and arylsulfatase A and the severity of the resulting lysosomal storage diseaseP Leinekugel, S Michel, E Conzelmann, et al.
Cellular and Molecular Biology (Noisy-Le-Grand, France)|December 10, 1998
Impairment of endothelial function induced by glyc-oxidized lipoprotein a [Lp(a)]J Galle, B Winner, E Conzelmann, et al.
European Journal of Biochemistry|August 1, 1995
Purification and characterization of an alpha-methylacyl-CoA racemase from human liverW Schmitz, C Albers, R Fingerhut, et al.
Hoppe-Seyler'S Zeitschrift Fur Physiologische Chemie|July 1, 1983
Activating proteins for ganglioside GM2 degradation by beta-hexosaminidase isoenzymes in tissue extracts from different speciesJ Burg, A Banerjee, E Conzelmann, et al.
European Journal of Biochemistry|April 1, 1982
Complexing of glycolipids and their transfer between membranes by the activator protein for degradation of lysosomal ganglioside GM2E Conzelmann, J Burg, G Stephan, et al.
American Journal of Human Genetics|September 1, 1983
Ganglioside GM2 N-acetyl-beta-D-galactosaminidase activity in cultured fibroblasts of late-infantile and adult GM2 gangliosidosis patients and of healthy probands with low hexosaminidase levelE Conzelmann, H J Kytzia, R Navon, et al.
Journal of Inherited Metabolic Disease|January 1, 1994
Impaired degradation of phytanic acid in cells from patients with mitochondriopathies: evidence for the involvement of ETF and the respiratory chain in phytanic acid alpha-oxidationR Fingerhut, W Schmitz, B Garavaglia, et al.
Biological Chemistry Hoppe-Seyler|March 1, 1986
Occurrence of lysoganglioside lyso-GM2 (II3-Neu5Ac-gangliotriaosylsphingosine) in GM2 gangliosidosis brainS Neuenhofer, E Conzelmann, G Schwarzmann, et al.
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