Jove
Visualize
Contact Us
JoVE
x logofacebook logolinkedin logoyoutube logo
ABOUT JoVE
OverviewLeadershipBlogJoVE Help Center
AUTHORS
Publishing ProcessEditorial BoardScope & PoliciesPeer ReviewFAQSubmit
LIBRARIANS
TestimonialsSubscriptionsAccessResourcesLibrary Advisory BoardFAQ
RESEARCH
JoVE JournalMethods CollectionsJoVE Encyclopedia of ExperimentsArchive
EDUCATION
JoVE CoreJoVE BusinessJoVE Science EducationJoVE Lab ManualFaculty Resource CenterFaculty Site
Terms & Conditions of Use
Privacy Policy
Policies

Filters

Felix Distelmaier

Showing results (81-90 of 151) with videos related to

Pageof 16
Sort By:
Neuropediatrics|May 23, 2022
Recognizable Pattern of Arthrogryposis and Congenital Myopathy Caused by the Recurrent TTN Metatranscript-only c.39974-11T > G Splice VariantLuisa Averdunk, Sandra Donkervoort, Denise Horn, et al.
European Journal of Paediatric Neurology : EJPN : Official Journal of the European Paediatric Neurology Society|September 26, 2022
Mitochondrial diseases mimicking autoimmune diseases of the CNS and good response to steroids initiallyAdela Della Marina, Annikki Bertolini, Andreas Wegener-Panzer, et al.
Brain : a Journal of Neurology|January 22, 2026
Successful treatment of neonatal COQ2 deficiency with 4-hydroxybenzoic acidJuliane Münch, Thomas Strahleck, Annette Seibt, et al.
Molecular Biology of the Cell|June 26, 2009
Human Golgi antiapoptotic protein modulates intracellular calcium fluxesFabrizio de Mattia, Caroline Gubser, Michiel M T van Dommelen, et al.
EMBO Molecular Medicine|November 19, 2016
CoQ deficiency causes disruption of mitochondrial sulfide oxidation, a new pathomechanism associated with this syndromeMarta Luna-Sánchez, Agustín Hidalgo-Gutiérrez, Tatjana M Hildebrandt, et al.
American Journal of Human Genetics|June 3, 2008
NDUFA2 complex I mutation leads to Leigh diseaseSaskia J G Hoefs, Cindy E J Dieteren, Felix Distelmaier, et al.
Brain : a Journal of Neurology|December 3, 2015
Human thioredoxin 2 deficiency impairs mitochondrial redox homeostasis and causes early-onset neurodegenerationEliska Holzerova, Katharina Danhauser, Tobias B Haack, et al.
Genetics in Medicine : Official Journal of the American College of Medical Genetics|January 10, 2026
Tyrosine supplementation with high-protein diet as a therapeutic strategy for YARS1 deficiencyLuisa Averdunk, Karin Konzett, Hanna Mandel, et al.
Movement Disorders : Official Journal of the Movement Disorder Society|September 1, 2022
Bi-Allelic COQ4 Variants Cause Adult-Onset Ataxia-Spasticity Spectrum DiseaseIsabell Cordts, Luisa Semmler, Jannik Prasuhn, et al.
Brain : a Journal of Neurology|September 10, 2025
Preclinical and first-in-human evidence of 4-hydroxybenzoic acid for mitochondrial COQ2 deficiencyFelix Distelmaier, Julia Corral-Sarasa, Laura Jiménez-Sánchez, et al.
Pageof 16

Showing results (81-90 of 151) with videos related to

Sort By:
Pageof 16
Neuropediatrics|May 23, 2022
Recognizable Pattern of Arthrogryposis and Congenital Myopathy Caused by the Recurrent TTN Metatranscript-only c.39974-11T > G Splice VariantLuisa Averdunk, Sandra Donkervoort, Denise Horn, et al.
European Journal of Paediatric Neurology : EJPN : Official Journal of the European Paediatric Neurology Society|September 26, 2022
Mitochondrial diseases mimicking autoimmune diseases of the CNS and good response to steroids initiallyAdela Della Marina, Annikki Bertolini, Andreas Wegener-Panzer, et al.
Brain : a Journal of Neurology|January 22, 2026
Successful treatment of neonatal COQ2 deficiency with 4-hydroxybenzoic acidJuliane Münch, Thomas Strahleck, Annette Seibt, et al.
Molecular Biology of the Cell|June 26, 2009
Human Golgi antiapoptotic protein modulates intracellular calcium fluxesFabrizio de Mattia, Caroline Gubser, Michiel M T van Dommelen, et al.
EMBO Molecular Medicine|November 19, 2016
CoQ deficiency causes disruption of mitochondrial sulfide oxidation, a new pathomechanism associated with this syndromeMarta Luna-Sánchez, Agustín Hidalgo-Gutiérrez, Tatjana M Hildebrandt, et al.
American Journal of Human Genetics|June 3, 2008
NDUFA2 complex I mutation leads to Leigh diseaseSaskia J G Hoefs, Cindy E J Dieteren, Felix Distelmaier, et al.
Brain : a Journal of Neurology|December 3, 2015
Human thioredoxin 2 deficiency impairs mitochondrial redox homeostasis and causes early-onset neurodegenerationEliska Holzerova, Katharina Danhauser, Tobias B Haack, et al.
Genetics in Medicine : Official Journal of the American College of Medical Genetics|January 10, 2026
Tyrosine supplementation with high-protein diet as a therapeutic strategy for YARS1 deficiencyLuisa Averdunk, Karin Konzett, Hanna Mandel, et al.
Movement Disorders : Official Journal of the Movement Disorder Society|September 1, 2022
Bi-Allelic COQ4 Variants Cause Adult-Onset Ataxia-Spasticity Spectrum DiseaseIsabell Cordts, Luisa Semmler, Jannik Prasuhn, et al.
Brain : a Journal of Neurology|September 10, 2025
Preclinical and first-in-human evidence of 4-hydroxybenzoic acid for mitochondrial COQ2 deficiencyFelix Distelmaier, Julia Corral-Sarasa, Laura Jiménez-Sánchez, et al.
Pageof 16