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Frances M Platt

Showing results (41-50 of 193) with videos related to

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The Journal of Biological Chemistry|July 21, 2004
Inhibition of glucosylceramide synthase does not reverse drug resistance in cancer cellsEdward Norris-Cervetto, Richard Callaghan, Frances M Platt, et al.
Nature Reviews. Disease Primers|October 3, 2018
Lysosomal storage diseasesFrances M Platt, Alessandra d'Azzo, Beverly L Davidson, et al.
Nature Reviews. Disease Primers|May 19, 2019
Publisher Correction: Lysosomal storage diseasesFrances M Platt, Alessandra d'Azzo, Beverly L Davidson, et al.
Proceedings of the National Academy of Sciences of the United States of America|March 21, 2007
Normal development and function of invariant natural killer T cells in mice with isoglobotrihexosylceramide (iGb3) deficiencyStefan Porubsky, Anneliese O Speak, Bruno Luckow, et al.
Micropublication Biology|September 19, 2025
Dissecting the impact of N-acetylmannosamine (ManNAc) on ganglioside levels in a sialin-deficient cell modelMarya S Sabir, Marjan Huizing, William A Gahl, et al.
Philosophical Transactions of the Royal Society of London. Series B, Biological Sciences|June 14, 2003
Substrate reduction therapy in mouse models of the glycosphingolipidosesFrances M Platt, Mylvaganam Jeyakumar, Ulrika Andersson, et al.
The Journal of Biological Chemistry|May 21, 2003
Inhibition of calcium uptake via the sarco/endoplasmic reticulum Ca2+-ATPase in a mouse model of Sandhoff disease and prevention by treatment with N-butyldeoxynojirimycinDori Pelled, Emyr Lloyd-Evans, Christian Riebeling, et al.
Journal of Inherited Metabolic Disease|February 16, 2013
Cyclodextrin alleviates neuronal storage of cholesterol in Niemann-Pick C disease without evidence of detectable blood-brain barrier permeabilityCharles C Pontikis, Cristin D Davidson, Steven U Walkley, et al.
Wellcome Open Research|November 10, 2017
Case Report: Ursodeoxycholic acid treatment in Niemann-Pick disease type C; clinical experience in four casesWilliam R H Evans, Elena-Raluca Nicoli, Raymond Y Wang, et al.
Frontiers in Genetics|September 20, 2021
GM1 Gangliosidosis-A Mini-ReviewElena-Raluca Nicoli, Ida Annunziata, Alessandra d'Azzo, et al.
Pageof 20

Showing results (41-50 of 193) with videos related to

Sort By:
Pageof 20
The Journal of Biological Chemistry|July 21, 2004
Inhibition of glucosylceramide synthase does not reverse drug resistance in cancer cellsEdward Norris-Cervetto, Richard Callaghan, Frances M Platt, et al.
Nature Reviews. Disease Primers|October 3, 2018
Lysosomal storage diseasesFrances M Platt, Alessandra d'Azzo, Beverly L Davidson, et al.
Nature Reviews. Disease Primers|May 19, 2019
Publisher Correction: Lysosomal storage diseasesFrances M Platt, Alessandra d'Azzo, Beverly L Davidson, et al.
Proceedings of the National Academy of Sciences of the United States of America|March 21, 2007
Normal development and function of invariant natural killer T cells in mice with isoglobotrihexosylceramide (iGb3) deficiencyStefan Porubsky, Anneliese O Speak, Bruno Luckow, et al.
Micropublication Biology|September 19, 2025
Dissecting the impact of N-acetylmannosamine (ManNAc) on ganglioside levels in a sialin-deficient cell modelMarya S Sabir, Marjan Huizing, William A Gahl, et al.
Philosophical Transactions of the Royal Society of London. Series B, Biological Sciences|June 14, 2003
Substrate reduction therapy in mouse models of the glycosphingolipidosesFrances M Platt, Mylvaganam Jeyakumar, Ulrika Andersson, et al.
The Journal of Biological Chemistry|May 21, 2003
Inhibition of calcium uptake via the sarco/endoplasmic reticulum Ca2+-ATPase in a mouse model of Sandhoff disease and prevention by treatment with N-butyldeoxynojirimycinDori Pelled, Emyr Lloyd-Evans, Christian Riebeling, et al.
Journal of Inherited Metabolic Disease|February 16, 2013
Cyclodextrin alleviates neuronal storage of cholesterol in Niemann-Pick C disease without evidence of detectable blood-brain barrier permeabilityCharles C Pontikis, Cristin D Davidson, Steven U Walkley, et al.
Wellcome Open Research|November 10, 2017
Case Report: Ursodeoxycholic acid treatment in Niemann-Pick disease type C; clinical experience in four casesWilliam R H Evans, Elena-Raluca Nicoli, Raymond Y Wang, et al.
Frontiers in Genetics|September 20, 2021
GM1 Gangliosidosis-A Mini-ReviewElena-Raluca Nicoli, Ida Annunziata, Alessandra d'Azzo, et al.
Pageof 20