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G A Jansen

Showing results (11-20 of 32) with videos related to

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Journal of Lipid Research|November 28, 1997
Phytanic acid alpha-oxidation: decarboxylation of 2-hydroxyphytanoyl-CoA to pristanic acid in human liverN M Verhoeven, R J Wanders, D S Schor, et al.
Journal of the Neurological Sciences|August 1, 1996
Evidence against increased oxidative stress in fibroblasts from patients with non-superoxide-dismutase-1 mutant familial amyotrophic lateral sclerosisG A Jansen, R J Wanders, G J Jöbsis, et al.
Advances in Experimental Medicine and Biology|March 10, 2000
Phytanoyl-CoA hydroxylase deficiency. Enzymological and molecular basis of classical Refsum diseaseG A Jansen, S Ferdinandusse, E M Hogenhout, et al.
Biochemical and Biophysical Research Communications|May 9, 2001
Identification of pristanal dehydrogenase activity in peroxisomes: conclusive evidence that the complete phytanic acid alpha-oxidation pathway is localized in peroxisomesG A Jansen, D M van den Brink, R Ofman, et al.
Clinica Chimica Acta; International Journal of Clinical Chemistry|June 6, 1998
Characterization of phytanoyl-Coenzyme A hydroxylase in human liver and activity measurements in patients with peroxisomal disordersG A Jansen, S J Mihalik, P A Watkins, et al.
Journal of Lipid Research|December 10, 1999
Phytanoyl-CoA hydroxylase from rat liver. Protein purification and cDNA cloning with implications for the subcellular localization of phytanic acid alpha-oxidationG A Jansen, R Ofman, S Denis, et al.
Biochemical and Biophysical Research Communications|December 4, 1996
Phytanoyl-CoA hydroxylase is present in human liver, located in peroxisomes, and deficient in Zellweger syndrome: direct, unequivocal evidence for the new, revised pathway of phytanic acid alpha-oxidation in humansG A Jansen, S J Mihalik, P A Watkins, et al.
Journal of Inherited Metabolic Disease|August 1, 1998
Molecular basis of Refsum disease: identification of new mutations in the phytanoyl-CoA hydroxylase cDNAG A Jansen, S Ferdinandusse, O H Skjeldal, et al.
Biochimica Et Biophysica Acta|October 16, 1999
Phytanic acid alpha-oxidation: identification of 2-hydroxyphytanoyl-CoA lyase in rat liver and its localisation in peroxisomesG A Jansen, N M Verhoeven, S Denis, et al.
Journal of Inherited Metabolic Disease|July 1, 1997
Phytanoyl-CoA hydroxylase is not only deficient in classical Refsum disease but also in rhizomelic chondrodysplasia punctataG A Jansen, S J Mihalik, P A Watkins, et al.
Pageof 4

Showing results (11-20 of 32) with videos related to

Sort By:
Pageof 4
Journal of Lipid Research|November 28, 1997
Phytanic acid alpha-oxidation: decarboxylation of 2-hydroxyphytanoyl-CoA to pristanic acid in human liverN M Verhoeven, R J Wanders, D S Schor, et al.
Journal of the Neurological Sciences|August 1, 1996
Evidence against increased oxidative stress in fibroblasts from patients with non-superoxide-dismutase-1 mutant familial amyotrophic lateral sclerosisG A Jansen, R J Wanders, G J Jöbsis, et al.
Advances in Experimental Medicine and Biology|March 10, 2000
Phytanoyl-CoA hydroxylase deficiency. Enzymological and molecular basis of classical Refsum diseaseG A Jansen, S Ferdinandusse, E M Hogenhout, et al.
Biochemical and Biophysical Research Communications|May 9, 2001
Identification of pristanal dehydrogenase activity in peroxisomes: conclusive evidence that the complete phytanic acid alpha-oxidation pathway is localized in peroxisomesG A Jansen, D M van den Brink, R Ofman, et al.
Clinica Chimica Acta; International Journal of Clinical Chemistry|June 6, 1998
Characterization of phytanoyl-Coenzyme A hydroxylase in human liver and activity measurements in patients with peroxisomal disordersG A Jansen, S J Mihalik, P A Watkins, et al.
Journal of Lipid Research|December 10, 1999
Phytanoyl-CoA hydroxylase from rat liver. Protein purification and cDNA cloning with implications for the subcellular localization of phytanic acid alpha-oxidationG A Jansen, R Ofman, S Denis, et al.
Biochemical and Biophysical Research Communications|December 4, 1996
Phytanoyl-CoA hydroxylase is present in human liver, located in peroxisomes, and deficient in Zellweger syndrome: direct, unequivocal evidence for the new, revised pathway of phytanic acid alpha-oxidation in humansG A Jansen, S J Mihalik, P A Watkins, et al.
Journal of Inherited Metabolic Disease|August 1, 1998
Molecular basis of Refsum disease: identification of new mutations in the phytanoyl-CoA hydroxylase cDNAG A Jansen, S Ferdinandusse, O H Skjeldal, et al.
Biochimica Et Biophysica Acta|October 16, 1999
Phytanic acid alpha-oxidation: identification of 2-hydroxyphytanoyl-CoA lyase in rat liver and its localisation in peroxisomesG A Jansen, N M Verhoeven, S Denis, et al.
Journal of Inherited Metabolic Disease|July 1, 1997
Phytanoyl-CoA hydroxylase is not only deficient in classical Refsum disease but also in rhizomelic chondrodysplasia punctataG A Jansen, S J Mihalik, P A Watkins, et al.
Pageof 4