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G Okun

Showing results (11-20 of 165) with videos related to

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Annals of Neurology|January 6, 2004
Pathomechanisms of neurodegeneration in glutaryl-CoA dehydrogenase deficiencyStefan Kölker, David M Koeller, Jürgen G Okun, et al.
Parkinsonism & Related Disorders|January 24, 2007
Nitrous oxide promotes hyperhomocysteinemia in levodopa treated ratsNils Henninger, Qi Wang, Jürgen G Okun, et al.
Journal of Inherited Metabolic Disease|December 25, 2004
S-Acetylglutathione normalizes intracellular glutathione content in cultured fibroblasts from patients with glutathione synthetase deficiencyJ G Okun, S Sauer, S Bähr, et al.
Journal of Inherited Metabolic Disease|July 30, 2010
Phenylalanine loading in pediatric patients with dopa-responsive dystonia: revised test protocol and pediatric cutoff valuesThomas Opladen, Jürgen G Okun, Peter Burgard, et al.
IUBMB Life|February 1, 2011
Ubiquinol-induced gene expression signatures are translated into altered parameters of erythropoiesis and reduced low density lipoprotein cholesterol levels in humansConstance Schmelzer, Petra Niklowitz, Jürgen G Okun, et al.
European Journal of Clinical Investigation|June 26, 2015
Ursodeoxycholyl Lysophosphatidylethanolamide modifies aberrant lipid profiles in NAFLDAnita Pathil, Gerhard Liebisch, Jürgen G Okun, et al.
Journal of Inherited Metabolic Disease|November 4, 2017
Impairment of astrocytic glutaminolysis in glutaric aciduria type IShoko Komatsuzaki, Raga Deepthi Ediga, Jürgen G Okun, et al.
Biochimica Et Biophysica Acta|June 28, 2008
Impact of short- and medium-chain organic acids, acylcarnitines, and acyl-CoAs on mitochondrial energy metabolismSven Wolfgang Sauer, Juergen G Okun, Georg F Hoffmann, et al.
Molecular Genetics and Metabolism|January 25, 2016
Co-expression of phenylalanine hydroxylase variants and effects of interallelic complementation on in vitro enzyme activity and genotype-phenotype correlationNan Shen, Caroline Heintz, Christian Thiel, et al.
Molecular Genetics and Metabolism|July 25, 2018
Relationship between genotype, phenylalanine hydroxylase expression and in vitro activity and metabolic phenotype in phenylketonuriaNastassja Himmelreich, Nan Shen, Jürgen G Okun, et al.
Pageof 17

Showing results (11-20 of 165) with videos related to

Sort By:
Pageof 17
Annals of Neurology|January 6, 2004
Pathomechanisms of neurodegeneration in glutaryl-CoA dehydrogenase deficiencyStefan Kölker, David M Koeller, Jürgen G Okun, et al.
Parkinsonism & Related Disorders|January 24, 2007
Nitrous oxide promotes hyperhomocysteinemia in levodopa treated ratsNils Henninger, Qi Wang, Jürgen G Okun, et al.
Journal of Inherited Metabolic Disease|December 25, 2004
S-Acetylglutathione normalizes intracellular glutathione content in cultured fibroblasts from patients with glutathione synthetase deficiencyJ G Okun, S Sauer, S Bähr, et al.
Journal of Inherited Metabolic Disease|July 30, 2010
Phenylalanine loading in pediatric patients with dopa-responsive dystonia: revised test protocol and pediatric cutoff valuesThomas Opladen, Jürgen G Okun, Peter Burgard, et al.
IUBMB Life|February 1, 2011
Ubiquinol-induced gene expression signatures are translated into altered parameters of erythropoiesis and reduced low density lipoprotein cholesterol levels in humansConstance Schmelzer, Petra Niklowitz, Jürgen G Okun, et al.
European Journal of Clinical Investigation|June 26, 2015
Ursodeoxycholyl Lysophosphatidylethanolamide modifies aberrant lipid profiles in NAFLDAnita Pathil, Gerhard Liebisch, Jürgen G Okun, et al.
Journal of Inherited Metabolic Disease|November 4, 2017
Impairment of astrocytic glutaminolysis in glutaric aciduria type IShoko Komatsuzaki, Raga Deepthi Ediga, Jürgen G Okun, et al.
Biochimica Et Biophysica Acta|June 28, 2008
Impact of short- and medium-chain organic acids, acylcarnitines, and acyl-CoAs on mitochondrial energy metabolismSven Wolfgang Sauer, Juergen G Okun, Georg F Hoffmann, et al.
Molecular Genetics and Metabolism|January 25, 2016
Co-expression of phenylalanine hydroxylase variants and effects of interallelic complementation on in vitro enzyme activity and genotype-phenotype correlationNan Shen, Caroline Heintz, Christian Thiel, et al.
Molecular Genetics and Metabolism|July 25, 2018
Relationship between genotype, phenylalanine hydroxylase expression and in vitro activity and metabolic phenotype in phenylketonuriaNastassja Himmelreich, Nan Shen, Jürgen G Okun, et al.
Pageof 17