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G P Mannaerts

Showing results (131-140 of 143) with videos related to

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Clinica Chimica Acta; International Journal of Clinical Chemistry|October 31, 1991
Accumulation and impaired in vivo metabolism of di- and trihydroxycholestanoic acid in two patientsR J Wanders, M Casteels, G P Mannaerts, et al.
European Journal of Clinical Investigation|July 28, 2001
Fibroblast studies documenting a case of peroxisomal 2-methylacyl-CoA racemase deficiency: possible link between racemase deficiency and malabsorption and vitamin K deficiencyP P Van Veldhoven, E Meyhi, R H Squires, et al.
Cellular and Molecular Life Sciences : CMLS|June 21, 2006
Thiamine pyrophosphate: an essential cofactor for the alpha-oxidation in mammals--implications for thiamine deficiencies?M Sniekers, V Foulon, G P Mannaerts, et al.
Lipids|June 1, 2001
Oxidative catabolism of alpha-tocopherol in rat liver microsomesH Van Houte, E De Hoffmann, P P Van Veldhoven, et al.
Neuromuscular Disorders : NMD|January 1, 1992
Neonatal seizures and severe hypotonia in a male infant suffering from a defect in peroxisomal beta-oxidationL Van Maldergem, M Espeel, R J Wanders, et al.
Journal of Inherited Metabolic Disease|January 1, 1991
Di- and trihydroxycholestanaemia in twin sistersR J Wanders, C W van Roermund, A Schelen, et al.
European Journal of Biochemistry|September 15, 1996
Further characterization of the peroxisomal 3-hydroxyacyl-CoA dehydrogenases from rat liver. Relationship between the different dehydrogenases and evidence that fatty acids and the C27 bile acids di- and tri-hydroxycoprostanic acids are metabolized by separate multifunctional proteinsM Dieuaide-Noubhani, D Novikov, E Baumgart, et al.
European Journal of Biochemistry|July 15, 1996
Rat pristanoyl-CoA oxidase. cDNA cloning and recognition of its C-terminal (SQL) by the peroxisomal-targeting signal 1 receptorJ C Vanhooren, M Fransen, B de Béthune, et al.
Proceedings of the National Academy of Sciences of the United States of America|November 26, 1996
Molecular characterization of the human peroxisomal branched-chain acyl-CoA oxidase: cDNA cloning, chromosomal assignment, tissue distribution, and evidence for the absence of the protein in Zellweger syndromeE Baumgart, J C Vanhooren, M Fransen, et al.
Journal of Neuropathology and Experimental Neurology|April 10, 2002
The neuronal migration defect in mice with Zellweger syndrome (Pex5 knockout) is not caused by the inactivity of peroxisomal beta-oxidationM Baes, P Gressens, S Huyghe, et al.
Pageof 15

Showing results (131-140 of 143) with videos related to

Sort By:
Pageof 15
Clinica Chimica Acta; International Journal of Clinical Chemistry|October 31, 1991
Accumulation and impaired in vivo metabolism of di- and trihydroxycholestanoic acid in two patientsR J Wanders, M Casteels, G P Mannaerts, et al.
European Journal of Clinical Investigation|July 28, 2001
Fibroblast studies documenting a case of peroxisomal 2-methylacyl-CoA racemase deficiency: possible link between racemase deficiency and malabsorption and vitamin K deficiencyP P Van Veldhoven, E Meyhi, R H Squires, et al.
Cellular and Molecular Life Sciences : CMLS|June 21, 2006
Thiamine pyrophosphate: an essential cofactor for the alpha-oxidation in mammals--implications for thiamine deficiencies?M Sniekers, V Foulon, G P Mannaerts, et al.
Lipids|June 1, 2001
Oxidative catabolism of alpha-tocopherol in rat liver microsomesH Van Houte, E De Hoffmann, P P Van Veldhoven, et al.
Neuromuscular Disorders : NMD|January 1, 1992
Neonatal seizures and severe hypotonia in a male infant suffering from a defect in peroxisomal beta-oxidationL Van Maldergem, M Espeel, R J Wanders, et al.
Journal of Inherited Metabolic Disease|January 1, 1991
Di- and trihydroxycholestanaemia in twin sistersR J Wanders, C W van Roermund, A Schelen, et al.
European Journal of Biochemistry|September 15, 1996
Further characterization of the peroxisomal 3-hydroxyacyl-CoA dehydrogenases from rat liver. Relationship between the different dehydrogenases and evidence that fatty acids and the C27 bile acids di- and tri-hydroxycoprostanic acids are metabolized by separate multifunctional proteinsM Dieuaide-Noubhani, D Novikov, E Baumgart, et al.
European Journal of Biochemistry|July 15, 1996
Rat pristanoyl-CoA oxidase. cDNA cloning and recognition of its C-terminal (SQL) by the peroxisomal-targeting signal 1 receptorJ C Vanhooren, M Fransen, B de Béthune, et al.
Proceedings of the National Academy of Sciences of the United States of America|November 26, 1996
Molecular characterization of the human peroxisomal branched-chain acyl-CoA oxidase: cDNA cloning, chromosomal assignment, tissue distribution, and evidence for the absence of the protein in Zellweger syndromeE Baumgart, J C Vanhooren, M Fransen, et al.
Journal of Neuropathology and Experimental Neurology|April 10, 2002
The neuronal migration defect in mice with Zellweger syndrome (Pex5 knockout) is not caused by the inactivity of peroxisomal beta-oxidationM Baes, P Gressens, S Huyghe, et al.
Pageof 15