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Gregory A Grabowski

Showing results (71-80 of 128) with videos related to

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Arteriosclerosis, Thrombosis, and Vascular Biology|March 31, 2018
LAL (Lysosomal Acid Lipase) Promotes Reverse Cholesterol Transport In Vitro and In VivoKristin L Bowden, Joshua A Dubland, Teddy Chan, et al.
Plos One|September 7, 2016
Progression of Behavioral and CNS Deficits in a Viable Murine Model of Chronic Neuronopathic Gaucher DiseaseMei Dai, Benjamin Liou, Brittany Swope, et al.
The Journal of Biological Chemistry|December 15, 2011
Ex vivo and in vivo effects of isofagomine on acid β-glucosidase variants and substrate levels in Gaucher diseaseYing Sun, Benjamin Liou, You-Hai Xu, et al.
Ebiomedicine|April 14, 2020
Systemic enzyme delivery by blood-brain barrier-penetrating SapC-DOPS nanovesicles for treatment of neuronopathic Gaucher diseaseYing Sun, Benjamin Liou, Zhengtao Chu, et al.
Plos One|March 23, 2013
Substrate compositional variation with tissue/region and Gba1 mutations in mouse models--implications for Gaucher diseaseYing Sun, Wujuan Zhang, You-Hai Xu, et al.
The Journal of Biological Chemistry|March 13, 2009
Acid beta-glucosidase 1 counteracts p38delta-dependent induction of interleukin-6: possible role for ceramide as an anti-inflammatory lipidKazuyuki Kitatani, Kely Sheldon, Viviana Anelli, et al.
Plos One|January 1, 2015
Ubiquitous transgene expression of the glucosylceramide-synthesizing enzyme accelerates glucosylceramide accumulation and storage cells in a Gaucher disease mouse modelSonya Barnes, You-Hai Xu, Wujuan Zhang, et al.
Molecular Genetics and Metabolism|March 20, 2025
Challenges in Gaucher disease: Perspectives from an expert panelGregory A Grabowski, Priya S Kishnani, Roy N Alcalay, et al.
Plos One|August 28, 2015
Activation of p38 Mitogen-Activated Protein Kinase in Gaucher's DiseaseKazuyuki Kitatani, Masayuki Wada, David Perry, et al.
The Journal of Neuroscience : the Official Journal of the Society for Neuroscience|February 21, 2015
Spiral ganglion degeneration and hearing loss as a consequence of satellite cell death in saposin B-deficient miceOmar Akil, Ying Sun, Sarath Vijayakumar, et al.
Pageof 13

Showing results (71-80 of 128) with videos related to

Sort By:
Pageof 13
Arteriosclerosis, Thrombosis, and Vascular Biology|March 31, 2018
LAL (Lysosomal Acid Lipase) Promotes Reverse Cholesterol Transport In Vitro and In VivoKristin L Bowden, Joshua A Dubland, Teddy Chan, et al.
Plos One|September 7, 2016
Progression of Behavioral and CNS Deficits in a Viable Murine Model of Chronic Neuronopathic Gaucher DiseaseMei Dai, Benjamin Liou, Brittany Swope, et al.
The Journal of Biological Chemistry|December 15, 2011
Ex vivo and in vivo effects of isofagomine on acid β-glucosidase variants and substrate levels in Gaucher diseaseYing Sun, Benjamin Liou, You-Hai Xu, et al.
Ebiomedicine|April 14, 2020
Systemic enzyme delivery by blood-brain barrier-penetrating SapC-DOPS nanovesicles for treatment of neuronopathic Gaucher diseaseYing Sun, Benjamin Liou, Zhengtao Chu, et al.
Plos One|March 23, 2013
Substrate compositional variation with tissue/region and Gba1 mutations in mouse models--implications for Gaucher diseaseYing Sun, Wujuan Zhang, You-Hai Xu, et al.
The Journal of Biological Chemistry|March 13, 2009
Acid beta-glucosidase 1 counteracts p38delta-dependent induction of interleukin-6: possible role for ceramide as an anti-inflammatory lipidKazuyuki Kitatani, Kely Sheldon, Viviana Anelli, et al.
Plos One|January 1, 2015
Ubiquitous transgene expression of the glucosylceramide-synthesizing enzyme accelerates glucosylceramide accumulation and storage cells in a Gaucher disease mouse modelSonya Barnes, You-Hai Xu, Wujuan Zhang, et al.
Molecular Genetics and Metabolism|March 20, 2025
Challenges in Gaucher disease: Perspectives from an expert panelGregory A Grabowski, Priya S Kishnani, Roy N Alcalay, et al.
Plos One|August 28, 2015
Activation of p38 Mitogen-Activated Protein Kinase in Gaucher's DiseaseKazuyuki Kitatani, Masayuki Wada, David Perry, et al.
The Journal of Neuroscience : the Official Journal of the Society for Neuroscience|February 21, 2015
Spiral ganglion degeneration and hearing loss as a consequence of satellite cell death in saposin B-deficient miceOmar Akil, Ying Sun, Sarath Vijayakumar, et al.
Pageof 13