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Gregory A Grabowski

Showing results (81-90 of 128) with videos related to

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Journal of Lipid Research|April 17, 2008
Wolman disease/cholesteryl ester storage disease: efficacy of plant-produced human lysosomal acid lipase in miceHong Du, Terri L Cameron, Stephen J Garger, et al.
The Journal of Biological Chemistry|March 13, 2009
Involvement of acid beta-glucosidase 1 in the salvage pathway of ceramide formationKazuyuki Kitatani, Kely Sheldon, Vinodh Rajagopalan, et al.
Cells|September 28, 2021
Substrate Reduction Therapy Reverses Mitochondrial, mTOR, and Autophagy Alterations in a Cell Model of Gaucher DiseaseYanyan Peng, Benjamin Liou, Yi Lin, et al.
Scientific Reports|April 5, 2019
Combination of acid β-glucosidase mutation and Saposin C deficiency in mice reveals Gba1 mutation dependent and tissue-specific disease phenotypeBenjamin Liou, Wujuan Zhang, Venette Fannin, et al.
The Journal of Gene Medicine|March 11, 2006
AAV8-mediated expression of glucocerebrosidase ameliorates the storage pathology in the visceral organs of a mouse model of Gaucher diseaseKerry Anne McEachern, Jennifer B Nietupski, Wei-Lien Chuang, et al.
Seminars in Hematology|October 7, 2004
Therapeutic goals in the treatment of Gaucher diseaseGregory M Pastores, Neal J Weinreb, Hans Aerts, et al.
Cell|June 25, 2011
Gaucher disease glucocerebrosidase and α-synuclein form a bidirectional pathogenic loop in synucleinopathiesJoseph R Mazzulli, You-Hai Xu, Ying Sun, et al.
Journal of Lipid Research|December 3, 2013
Endogenous β-glucocerebrosidase activity in Abca12⁻/⁻epidermis elevates ceramide levels after topical lipid application but does not restore barrier functionJorge F Haller, Paul Cavallaro, Nicholas J Hernandez, et al.
BMC Genomics|January 13, 2011
Global gene expression profile progression in Gaucher disease mouse modelsYou-Hai Xu, Li Jia, Brian Quinn, et al.
Molecular Genetics and Metabolism|May 20, 2014
Reversal of advanced disease in lysosomal acid lipase deficient mice: a model for lysosomal acid lipase deficiency diseaseYing Sun, You-Hai Xu, Hong Du, et al.
Pageof 13

Showing results (81-90 of 128) with videos related to

Sort By:
Pageof 13
Journal of Lipid Research|April 17, 2008
Wolman disease/cholesteryl ester storage disease: efficacy of plant-produced human lysosomal acid lipase in miceHong Du, Terri L Cameron, Stephen J Garger, et al.
The Journal of Biological Chemistry|March 13, 2009
Involvement of acid beta-glucosidase 1 in the salvage pathway of ceramide formationKazuyuki Kitatani, Kely Sheldon, Vinodh Rajagopalan, et al.
Cells|September 28, 2021
Substrate Reduction Therapy Reverses Mitochondrial, mTOR, and Autophagy Alterations in a Cell Model of Gaucher DiseaseYanyan Peng, Benjamin Liou, Yi Lin, et al.
Scientific Reports|April 5, 2019
Combination of acid β-glucosidase mutation and Saposin C deficiency in mice reveals Gba1 mutation dependent and tissue-specific disease phenotypeBenjamin Liou, Wujuan Zhang, Venette Fannin, et al.
The Journal of Gene Medicine|March 11, 2006
AAV8-mediated expression of glucocerebrosidase ameliorates the storage pathology in the visceral organs of a mouse model of Gaucher diseaseKerry Anne McEachern, Jennifer B Nietupski, Wei-Lien Chuang, et al.
Seminars in Hematology|October 7, 2004
Therapeutic goals in the treatment of Gaucher diseaseGregory M Pastores, Neal J Weinreb, Hans Aerts, et al.
Cell|June 25, 2011
Gaucher disease glucocerebrosidase and α-synuclein form a bidirectional pathogenic loop in synucleinopathiesJoseph R Mazzulli, You-Hai Xu, Ying Sun, et al.
Journal of Lipid Research|December 3, 2013
Endogenous β-glucocerebrosidase activity in Abca12⁻/⁻epidermis elevates ceramide levels after topical lipid application but does not restore barrier functionJorge F Haller, Paul Cavallaro, Nicholas J Hernandez, et al.
BMC Genomics|January 13, 2011
Global gene expression profile progression in Gaucher disease mouse modelsYou-Hai Xu, Li Jia, Brian Quinn, et al.
Molecular Genetics and Metabolism|May 20, 2014
Reversal of advanced disease in lysosomal acid lipase deficient mice: a model for lysosomal acid lipase deficiency diseaseYing Sun, You-Hai Xu, Hong Du, et al.
Pageof 13