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Jan Smeitink

Showing results (41-50 of 74) with videos related to

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American Journal of Medical Genetics. Part A|March 15, 2006
Clinical and biochemical characteristics in patients with a high mutant load of the mitochondrial T8993G/C mutationsEva Morava, Richard J Rodenburg, Frans Hol, et al.
JIMD Reports|July 14, 2021
Human d-lactate dehydrogenase deficiency by <i>LDHD</i> mutation in a patient with neurological manifestations and mitochondrial complex IV deficiencyAnna Ka-Yee Kwong, Sheila Suet-Na Wong, Richard J T Rodenburg, et al.
European Journal of Pediatrics|May 29, 2004
Congenital hypertrophic cardiomyopathy, cataract, mitochondrial myopathy and defective oxidative phosphorylation in two siblings with Sengers-like syndromeEva Morava, Rob Sengers, Henk Ter Laak, et al.
Scientific Reports|September 24, 2020
Oxidative switch drives mitophagy defects in dopaminergic parkin mutant patient neuronsAurelie Schwartzentruber, Camilla Boschian, Fernanda Martins Lopes, et al.
Journal of Inherited Metabolic Disease|March 14, 2018
Quantification of gait in children with mitochondrial diseaseSaskia Koene, Niki M Stolwijk, Rob Ramakers, et al.
Epilepsia Open|August 11, 2021
High FGF-21 level in a cohort of 22 patients with Dravet Syndrome-Possible relationship with the disease outcomesAnna Ka-Yee Kwong, Virginia Chun-Nei Wong, Sheila Suet-Na Wong, et al.
The Biochemical Journal|January 13, 2006
Metallothionein isoform 2A expression is inducible and protects against ROS-mediated cell death in rotenone-treated HeLa cellsFimmie Reinecke, Oksana Levanets, Yolanda Olivier, et al.
European Journal of Pediatrics|August 20, 2003
Leigh syndrome due to compound heterozygosity of dihydrolipoamide dehydrogenase gene mutations. Description of the first E3 splice site mutationOlga Grafakou, Konrad Oexle, Lambert van den Heuvel, et al.
Journal of Child Neurology|April 16, 2003
Application of a ketogenic diet in children with autistic behavior: pilot studyAthanasios Evangeliou, Ioannis Vlachonikolis, Helen Mihailidou, et al.
Clinical Pharmacology and Therapeutics|July 31, 2018
The KHENERGY Study: Safety and Efficacy of KH176 in Mitochondrial m.3243A>G Spectrum DisordersMirian C H Janssen, Saskia Koene, Paul de Laat, et al.
Pageof 8

Showing results (41-50 of 74) with videos related to

Sort By:
Pageof 8
American Journal of Medical Genetics. Part A|March 15, 2006
Clinical and biochemical characteristics in patients with a high mutant load of the mitochondrial T8993G/C mutationsEva Morava, Richard J Rodenburg, Frans Hol, et al.
JIMD Reports|July 14, 2021
Human d-lactate dehydrogenase deficiency by <i>LDHD</i> mutation in a patient with neurological manifestations and mitochondrial complex IV deficiencyAnna Ka-Yee Kwong, Sheila Suet-Na Wong, Richard J T Rodenburg, et al.
European Journal of Pediatrics|May 29, 2004
Congenital hypertrophic cardiomyopathy, cataract, mitochondrial myopathy and defective oxidative phosphorylation in two siblings with Sengers-like syndromeEva Morava, Rob Sengers, Henk Ter Laak, et al.
Scientific Reports|September 24, 2020
Oxidative switch drives mitophagy defects in dopaminergic parkin mutant patient neuronsAurelie Schwartzentruber, Camilla Boschian, Fernanda Martins Lopes, et al.
Journal of Inherited Metabolic Disease|March 14, 2018
Quantification of gait in children with mitochondrial diseaseSaskia Koene, Niki M Stolwijk, Rob Ramakers, et al.
Epilepsia Open|August 11, 2021
High FGF-21 level in a cohort of 22 patients with Dravet Syndrome-Possible relationship with the disease outcomesAnna Ka-Yee Kwong, Virginia Chun-Nei Wong, Sheila Suet-Na Wong, et al.
The Biochemical Journal|January 13, 2006
Metallothionein isoform 2A expression is inducible and protects against ROS-mediated cell death in rotenone-treated HeLa cellsFimmie Reinecke, Oksana Levanets, Yolanda Olivier, et al.
European Journal of Pediatrics|August 20, 2003
Leigh syndrome due to compound heterozygosity of dihydrolipoamide dehydrogenase gene mutations. Description of the first E3 splice site mutationOlga Grafakou, Konrad Oexle, Lambert van den Heuvel, et al.
Journal of Child Neurology|April 16, 2003
Application of a ketogenic diet in children with autistic behavior: pilot studyAthanasios Evangeliou, Ioannis Vlachonikolis, Helen Mihailidou, et al.
Clinical Pharmacology and Therapeutics|July 31, 2018
The KHENERGY Study: Safety and Efficacy of KH176 in Mitochondrial m.3243A>G Spectrum DisordersMirian C H Janssen, Saskia Koene, Paul de Laat, et al.
Pageof 8