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Jerry Vockley

Showing results (71-80 of 293) with videos related to

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Molecular Genetics and Metabolism|April 5, 2022
Phenylketonuria oxidative stress and energy dysregulation: Emerging pathophysiological elements provide interventional opportunitySteven F Dobrowolski, Yu Leng Phua, Jerry Vockley, et al.
Molecular Genetics and Metabolism|August 5, 2019
Perspectives on urea cycle disorder management: Results of a clinician surveyGregory M Enns, Marty H Porter, Megan Francis-Sedlak, et al.
The Journal of Biological Chemistry|October 7, 2004
Leaky beta-oxidation of a trans-fatty acid: incomplete beta-oxidation of elaidic acid is due to the accumulation of 5-trans-tetradecenoyl-CoA and its hydrolysis and conversion to 5-trans-tetradecenoylcarnitine in the matrix of rat mitochondriaWenfeng Yu, Xiquan Liang, Regina E Ensenauer, et al.
The Journal of Biological Chemistry|July 29, 2010
Evidence for physical association of mitochondrial fatty acid oxidation and oxidative phosphorylation complexesYudong Wang, Al-Walid Mohsen, Stephanie J Mihalik, et al.
Molecular Genetics and Metabolism|May 28, 2023
Challenges and strategies for clinical trials in propionic and methylmalonic acidemiasJerry Vockley, Barbara Burton, Agnieszka Jurecka, et al.
Current Protocols|February 23, 2026
Correction: Preparation of Vitrified Mammalian Cells for In Situ Cryo-Electron TomographyEva Martin-Solana, Sonia Frendi, Jiying Ning, et al.
Molecular Neurobiology|September 9, 2024
Disruption of Mitochondrial Quality Control in Inherited Metabolic DisordersManuela Bianchin Marcuzzo, Josyane de Andrade Silveira, Emílio L Streck, et al.
Current Protocols|October 28, 2025
Preparation of Vitrified Mammalian Cells for In Situ Cryo-Electron TomographyEva Martin-Solana, Sonia Frendi, Jiying Ning, et al.
Journal of Inherited Metabolic Disease|February 26, 2019
Response to Letter to the editorMelanie B Gillingham, Stephen B Heitner, Michael R Lasarev, et al.
Frontiers in Genetics|February 15, 2021
Physiological Perspectives on the Use of Triheptanoin as Anaplerotic Therapy for Long Chain Fatty Acid Oxidation DisordersEvgenia Sklirou, Ahmad N Alodaib, Steven F Dobrowolski, et al.
Pageof 30

Showing results (71-80 of 293) with videos related to

Sort By:
Pageof 30
Molecular Genetics and Metabolism|April 5, 2022
Phenylketonuria oxidative stress and energy dysregulation: Emerging pathophysiological elements provide interventional opportunitySteven F Dobrowolski, Yu Leng Phua, Jerry Vockley, et al.
Molecular Genetics and Metabolism|August 5, 2019
Perspectives on urea cycle disorder management: Results of a clinician surveyGregory M Enns, Marty H Porter, Megan Francis-Sedlak, et al.
The Journal of Biological Chemistry|October 7, 2004
Leaky beta-oxidation of a trans-fatty acid: incomplete beta-oxidation of elaidic acid is due to the accumulation of 5-trans-tetradecenoyl-CoA and its hydrolysis and conversion to 5-trans-tetradecenoylcarnitine in the matrix of rat mitochondriaWenfeng Yu, Xiquan Liang, Regina E Ensenauer, et al.
The Journal of Biological Chemistry|July 29, 2010
Evidence for physical association of mitochondrial fatty acid oxidation and oxidative phosphorylation complexesYudong Wang, Al-Walid Mohsen, Stephanie J Mihalik, et al.
Molecular Genetics and Metabolism|May 28, 2023
Challenges and strategies for clinical trials in propionic and methylmalonic acidemiasJerry Vockley, Barbara Burton, Agnieszka Jurecka, et al.
Current Protocols|February 23, 2026
Correction: Preparation of Vitrified Mammalian Cells for In Situ Cryo-Electron TomographyEva Martin-Solana, Sonia Frendi, Jiying Ning, et al.
Molecular Neurobiology|September 9, 2024
Disruption of Mitochondrial Quality Control in Inherited Metabolic DisordersManuela Bianchin Marcuzzo, Josyane de Andrade Silveira, Emílio L Streck, et al.
Current Protocols|October 28, 2025
Preparation of Vitrified Mammalian Cells for In Situ Cryo-Electron TomographyEva Martin-Solana, Sonia Frendi, Jiying Ning, et al.
Journal of Inherited Metabolic Disease|February 26, 2019
Response to Letter to the editorMelanie B Gillingham, Stephen B Heitner, Michael R Lasarev, et al.
Frontiers in Genetics|February 15, 2021
Physiological Perspectives on the Use of Triheptanoin as Anaplerotic Therapy for Long Chain Fatty Acid Oxidation DisordersEvgenia Sklirou, Ahmad N Alodaib, Steven F Dobrowolski, et al.
Pageof 30