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Jonathan D Cooper

Showing results (61-70 of 144) with videos related to

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Molecular Therapy. Methods & Clinical Development|August 14, 2018
Genetically Corrected iPSC-Derived Neural Stem Cell Grafts Deliver Enzyme Replacement to Affect CNS Disease in Sanfilippo B MiceDon Clarke, Yewande Pearse, Shih-Hsin Kan, et al.
Acta Neuropathologica Communications|August 10, 2018
Compromised astrocyte function and survival negatively impact neurons in infantile neuronal ceroid lipofuscinosisJenny Lange, Luke J Haslett, Emyr Lloyd-Evans, et al.
Annals of Neurology|February 28, 2012
Synergistic effects of central nervous system-directed gene therapy and bone marrow transplantation in the murine model of infantile neuronal ceroid lipofuscinosisShannon L Macauley, Marie S Roberts, Andrew M Wong, et al.
Journal of Neuropathology and Experimental Neurology|November 26, 2010
Distinct neuropathologic phenotypes after disrupting the chloride transport proteins ClC-6 or ClC-7/Ostm1Sarah N R Pressey, Kieran J O'Donnell, Tobias Stauber, et al.
Molecular Genetics and Metabolism|May 17, 2017
Partial rescue of neuropathology in the murine model of PKU following administration of recombinant phenylalanine ammonia lyase (pegvaliase)Marc Goldfinger, William L Zeile, Carley R Corado, et al.
Journal of Neuropathology and Experimental Neurology|November 16, 2011
Morphologic and functional correlates of synaptic pathology in the cathepsin D knockout mouse model of congenital neuronal ceroid lipofuscinosisSabine Koch, Svetlana M Molchanova, Ann K Wright, et al.
Plos One|April 27, 2012
Disruption of the autophagy-lysosome pathway is involved in neuropathology of the nclf mouse model of neuronal ceroid lipofuscinosisMelanie Thelen, Markus Damme, Markus Daμμe, et al.
Neurobiology of Disease|April 23, 2009
Progressive thalamocortical neuron loss in Cln5 deficient mice: Distinct effects in Finnish variant late infantile NCLCarina von Schantz, Catherine Kielar, Stine N Hansen, et al.
Brain Research|February 24, 2009
Cerebellar defects in a mouse model of juvenile neuronal ceroid lipofuscinosisJill M Weimer, Jared W Benedict, Amanda L Getty, et al.
Disease Models & Mechanisms|October 16, 2012
Exacerbated neuronal ceroid lipofuscinosis phenotype in Cln1/5 double-knockout miceTea Blom, Mia-Lisa Schmiedt, Andrew M Wong, et al.
Pageof 15

Showing results (61-70 of 144) with videos related to

Sort By:
Pageof 15
Molecular Therapy. Methods & Clinical Development|August 14, 2018
Genetically Corrected iPSC-Derived Neural Stem Cell Grafts Deliver Enzyme Replacement to Affect CNS Disease in Sanfilippo B MiceDon Clarke, Yewande Pearse, Shih-Hsin Kan, et al.
Acta Neuropathologica Communications|August 10, 2018
Compromised astrocyte function and survival negatively impact neurons in infantile neuronal ceroid lipofuscinosisJenny Lange, Luke J Haslett, Emyr Lloyd-Evans, et al.
Annals of Neurology|February 28, 2012
Synergistic effects of central nervous system-directed gene therapy and bone marrow transplantation in the murine model of infantile neuronal ceroid lipofuscinosisShannon L Macauley, Marie S Roberts, Andrew M Wong, et al.
Journal of Neuropathology and Experimental Neurology|November 26, 2010
Distinct neuropathologic phenotypes after disrupting the chloride transport proteins ClC-6 or ClC-7/Ostm1Sarah N R Pressey, Kieran J O'Donnell, Tobias Stauber, et al.
Molecular Genetics and Metabolism|May 17, 2017
Partial rescue of neuropathology in the murine model of PKU following administration of recombinant phenylalanine ammonia lyase (pegvaliase)Marc Goldfinger, William L Zeile, Carley R Corado, et al.
Journal of Neuropathology and Experimental Neurology|November 16, 2011
Morphologic and functional correlates of synaptic pathology in the cathepsin D knockout mouse model of congenital neuronal ceroid lipofuscinosisSabine Koch, Svetlana M Molchanova, Ann K Wright, et al.
Plos One|April 27, 2012
Disruption of the autophagy-lysosome pathway is involved in neuropathology of the nclf mouse model of neuronal ceroid lipofuscinosisMelanie Thelen, Markus Damme, Markus Daμμe, et al.
Neurobiology of Disease|April 23, 2009
Progressive thalamocortical neuron loss in Cln5 deficient mice: Distinct effects in Finnish variant late infantile NCLCarina von Schantz, Catherine Kielar, Stine N Hansen, et al.
Brain Research|February 24, 2009
Cerebellar defects in a mouse model of juvenile neuronal ceroid lipofuscinosisJill M Weimer, Jared W Benedict, Amanda L Getty, et al.
Disease Models & Mechanisms|October 16, 2012
Exacerbated neuronal ceroid lipofuscinosis phenotype in Cln1/5 double-knockout miceTea Blom, Mia-Lisa Schmiedt, Andrew M Wong, et al.
Pageof 15