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K Sandhoff

Showing results (81-90 of 256) with videos related to

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Human Genetics|January 1, 1984
Diagnosis of infantile and juvenile forms of GM2 gangliosidosis variant 0. Residual activities toward natural and different synthetic substratesH J Kytzia, U Hinrichs, K Sandhoff
Journal of Neurochemistry|April 1, 1992
Fractionation of primary cultured cerebellar neurons: distribution of sialyltransferases involved in ganglioside biosynthesisH Iber, G van Echten, K Sandhoff
Proceedings of the National Academy of Sciences of the United States of America|December 1, 1983
Tunicamycin inhibits ganglioside biosynthesis in rat liver Golgi apparatus by blocking sugar nucleotide transport across the membrane vesiclesH K Yusuf, G Pohlentz, K Sandhoff
Human Genetics|March 1, 1992
Quantitative correlation between the residual activity of beta-hexosaminidase A and arylsulfatase A and the severity of the resulting lysosomal storage diseaseP Leinekugel, S Michel, E Conzelmann, et al.
Biological Chemistry|September 15, 2000
Characterization of regulatory elements in the 5'-flanking region of the GM2 activator geneU Schepers, T Lemm, V Herzog, et al.
FEBS Letters|September 23, 1991
A mutation in the gene of a glycolipid-binding protein (GM2 activator) that causes GM2-gangliosidosis variant ABM Schröder, D Schnabel, K Suzuki, et al.
Advances in Experimental Medicine and Biology|January 1, 1980
Sialidase in brain and fibroblasts in three patients with different types of sialidosisB Pallmann, K Sandhoff, B Berra, et al.
European Journal of Biochemistry|September 15, 1987
Substrate specificity of GM2 and GD3 synthase of Golgi vesicles derived from rat liverD Klein, G Pohlentz, G Schwarzmann, et al.
The Journal of Histochemistry and Cytochemistry : Official Journal of the Histochemistry Society|July 29, 1999
Intracellular distribution of a biotin-labeled ganglioside, GM1, by immunoelectron microscopy after endocytosis in fibroblastsW Möbius, V Herzog, K Sandhoff, et al.
Chemistry and Physics of Lipids|March 28, 1997
Synthesis and mass spectrometric characterization of digoxigenin and biotin labeled ganglioside GM1 and their uptake by and metabolism in cultured cellsB Albrecht, G Pohlentz, K Sandhoff, et al.
Pageof 26

Showing results (81-90 of 256) with videos related to

Sort By:
Pageof 26
Human Genetics|January 1, 1984
Diagnosis of infantile and juvenile forms of GM2 gangliosidosis variant 0. Residual activities toward natural and different synthetic substratesH J Kytzia, U Hinrichs, K Sandhoff
Journal of Neurochemistry|April 1, 1992
Fractionation of primary cultured cerebellar neurons: distribution of sialyltransferases involved in ganglioside biosynthesisH Iber, G van Echten, K Sandhoff
Proceedings of the National Academy of Sciences of the United States of America|December 1, 1983
Tunicamycin inhibits ganglioside biosynthesis in rat liver Golgi apparatus by blocking sugar nucleotide transport across the membrane vesiclesH K Yusuf, G Pohlentz, K Sandhoff
Human Genetics|March 1, 1992
Quantitative correlation between the residual activity of beta-hexosaminidase A and arylsulfatase A and the severity of the resulting lysosomal storage diseaseP Leinekugel, S Michel, E Conzelmann, et al.
Biological Chemistry|September 15, 2000
Characterization of regulatory elements in the 5'-flanking region of the GM2 activator geneU Schepers, T Lemm, V Herzog, et al.
FEBS Letters|September 23, 1991
A mutation in the gene of a glycolipid-binding protein (GM2 activator) that causes GM2-gangliosidosis variant ABM Schröder, D Schnabel, K Suzuki, et al.
Advances in Experimental Medicine and Biology|January 1, 1980
Sialidase in brain and fibroblasts in three patients with different types of sialidosisB Pallmann, K Sandhoff, B Berra, et al.
European Journal of Biochemistry|September 15, 1987
Substrate specificity of GM2 and GD3 synthase of Golgi vesicles derived from rat liverD Klein, G Pohlentz, G Schwarzmann, et al.
The Journal of Histochemistry and Cytochemistry : Official Journal of the Histochemistry Society|July 29, 1999
Intracellular distribution of a biotin-labeled ganglioside, GM1, by immunoelectron microscopy after endocytosis in fibroblastsW Möbius, V Herzog, K Sandhoff, et al.
Chemistry and Physics of Lipids|March 28, 1997
Synthesis and mass spectrometric characterization of digoxigenin and biotin labeled ganglioside GM1 and their uptake by and metabolism in cultured cellsB Albrecht, G Pohlentz, K Sandhoff, et al.
Pageof 26