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Kim M Keeling

Showing results (21-30 of 33) with videos related to

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Molecular Genetics and Metabolism|November 8, 2011
The designer aminoglycoside NB84 significantly reduces glycosaminoglycan accumulation associated with MPS I-H in the Idua-W392X mouseDan Wang, Valery Belakhov, Jeyakumar Kandasamy, et al.
Molecular Genetics and Metabolism|January 14, 2014
Long-term nonsense suppression therapy moderates MPS I-H disease progressionGwen Gunn, Yanying Dai, Ming Du, et al.
Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society|September 27, 2025
Identity, functional consequences, and context effects of amino acids inserted during suppression of CFTR nonsense mutationsKari Thrasher, Jianguo Chen, Lianwu Fu, et al.
Plos One|April 18, 2013
Attenuation of nonsense-mediated mRNA decay enhances in vivo nonsense suppressionKim M Keeling, Dan Wang, Yanying Dai, et al.
Molecular Cell|June 10, 2008
Distinct eRF3 requirements suggest alternate eRF1 conformations mediate peptide release during eukaryotic translation terminationHua Fan-Minogue, Ming Du, Andrey V Pisarev, et al.
American Journal of Physiology. Lung Cellular and Molecular Physiology|April 4, 2023
The synthetic aminoglycoside ELX-02 induces readthrough of G550X-CFTR producing superfunctional protein that can be further enhanced by CFTR modulatorsJianguo Chen, Kari Thrasher, Lianwu Fu, et al.
Molecular Therapy. Nucleic Acids|May 15, 2020
Mutation-Directed Therapeutics for Neurofibromatosis Type IAndre Leier, David M Bedwell, Ann T Chen, et al.
Journal of Molecular Medicine (Berlin, Germany)|September 13, 2002
Aminoglycoside suppression of a premature stop mutation in a Cftr-/- mouse carrying a human CFTR-G542X transgeneMing Du, Julie R Jones, Jessica Lanier, et al.
Molecular Therapy. Oncology|April 6, 2026
Identification of small molecules that enhance aminoglycoside-mediated suppression of <i>CFTR</i> and <i>NF1</i> nonsense mutationsJoshua Sammons, Jianguo Chen, Kari Thrasher, et al.
Proceedings of the National Academy of Sciences of the United States of America|October 6, 2016
Ataluren stimulates ribosomal selection of near-cognate tRNAs to promote nonsense suppressionBijoyita Roy, Westley J Friesen, Yuki Tomizawa, et al.
Pageof 4

Showing results (21-30 of 33) with videos related to

Sort By:
Pageof 4
Molecular Genetics and Metabolism|November 8, 2011
The designer aminoglycoside NB84 significantly reduces glycosaminoglycan accumulation associated with MPS I-H in the Idua-W392X mouseDan Wang, Valery Belakhov, Jeyakumar Kandasamy, et al.
Molecular Genetics and Metabolism|January 14, 2014
Long-term nonsense suppression therapy moderates MPS I-H disease progressionGwen Gunn, Yanying Dai, Ming Du, et al.
Journal of Cystic Fibrosis : Official Journal of the European Cystic Fibrosis Society|September 27, 2025
Identity, functional consequences, and context effects of amino acids inserted during suppression of CFTR nonsense mutationsKari Thrasher, Jianguo Chen, Lianwu Fu, et al.
Plos One|April 18, 2013
Attenuation of nonsense-mediated mRNA decay enhances in vivo nonsense suppressionKim M Keeling, Dan Wang, Yanying Dai, et al.
Molecular Cell|June 10, 2008
Distinct eRF3 requirements suggest alternate eRF1 conformations mediate peptide release during eukaryotic translation terminationHua Fan-Minogue, Ming Du, Andrey V Pisarev, et al.
American Journal of Physiology. Lung Cellular and Molecular Physiology|April 4, 2023
The synthetic aminoglycoside ELX-02 induces readthrough of G550X-CFTR producing superfunctional protein that can be further enhanced by CFTR modulatorsJianguo Chen, Kari Thrasher, Lianwu Fu, et al.
Molecular Therapy. Nucleic Acids|May 15, 2020
Mutation-Directed Therapeutics for Neurofibromatosis Type IAndre Leier, David M Bedwell, Ann T Chen, et al.
Journal of Molecular Medicine (Berlin, Germany)|September 13, 2002
Aminoglycoside suppression of a premature stop mutation in a Cftr-/- mouse carrying a human CFTR-G542X transgeneMing Du, Julie R Jones, Jessica Lanier, et al.
Molecular Therapy. Oncology|April 6, 2026
Identification of small molecules that enhance aminoglycoside-mediated suppression of <i>CFTR</i> and <i>NF1</i> nonsense mutationsJoshua Sammons, Jianguo Chen, Kari Thrasher, et al.
Proceedings of the National Academy of Sciences of the United States of America|October 6, 2016
Ataluren stimulates ribosomal selection of near-cognate tRNAs to promote nonsense suppressionBijoyita Roy, Westley J Friesen, Yuki Tomizawa, et al.
Pageof 4