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L Vilarinho

Showing results (21-30 of 42) with videos related to

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Molecular Genetics and Metabolism|August 11, 2006
Overexpression of GAMT restores GAMT activity in primary GAMT-deficient fibroblastsL S Almeida, E H Rosenberg, C Martinez-Muñoz, et al.
Molecular Genetics and Metabolism|March 6, 2007
A prevalent pathogenic GAMT mutation (c.59G>C) in PortugalL S Almeida, L Vilarinho, P S Darmin, et al.
Brain & Development|June 1, 1997
L-2-Hydroxyglutaric aciduria: clinical, biochemical and magnetic resonance imaging in six Portuguese pediatric patientsC Barbot, I Fineza, L Diogo, et al.
Journal of Inherited Metabolic Disease|May 9, 2000
Multiple mtDNA deletions: clinical and molecular correlationsF M Santorelli, G De Joanna, C Casali, et al.
Molecular Genetics and Metabolism|August 17, 2004
The E37X is a common HMGCL mutation in Portuguese patients with 3-hydroxy-3-methylglutaric CoA lyase deficiencyM L Cardoso, M R Rodrigues, E Leão, et al.
Journal of Inherited Metabolic Disease|September 16, 2003
CblE type of homocystinuria: mild clinical phenotype in two patients homozygous for a novel mutation in the MTRR geneM A Vilaseca, L Vilarinho, P Zavadakova, et al.
Journal of Inherited Metabolic Disease|October 17, 2006
Mutational spectrum of classical galactosaemia in Spain and PortugalL Gort, M D Boleda, L Tyfield, et al.
The Journal of Biological Chemistry|May 25, 1991
A 3-base pair in-frame deletion of the phenylalanine hydroxylase gene results in a kinetic variant of phenylketonuriaC Caillaud, S Lyonnet, F Rey, et al.
Human Genetics|April 1, 1992
Linkage disequilibrium between phenylketonuria and RFLP haplotype 1 at the phenylalanine hydroxylase locus in PortugalC Caillaud, L Vilarinho, A Vilarinho, et al.
Journal of the Neurological Sciences|June 17, 1999
The mitochondrial DNA A3243G mutation in Portugal: clinical and molecular studies in 5 familiesL Vilarinho, F M Santorelli, I Coelho, et al.
Pageof 5

Showing results (21-30 of 42) with videos related to

Sort By:
Pageof 5
Molecular Genetics and Metabolism|August 11, 2006
Overexpression of GAMT restores GAMT activity in primary GAMT-deficient fibroblastsL S Almeida, E H Rosenberg, C Martinez-Muñoz, et al.
Molecular Genetics and Metabolism|March 6, 2007
A prevalent pathogenic GAMT mutation (c.59G>C) in PortugalL S Almeida, L Vilarinho, P S Darmin, et al.
Brain & Development|June 1, 1997
L-2-Hydroxyglutaric aciduria: clinical, biochemical and magnetic resonance imaging in six Portuguese pediatric patientsC Barbot, I Fineza, L Diogo, et al.
Journal of Inherited Metabolic Disease|May 9, 2000
Multiple mtDNA deletions: clinical and molecular correlationsF M Santorelli, G De Joanna, C Casali, et al.
Molecular Genetics and Metabolism|August 17, 2004
The E37X is a common HMGCL mutation in Portuguese patients with 3-hydroxy-3-methylglutaric CoA lyase deficiencyM L Cardoso, M R Rodrigues, E Leão, et al.
Journal of Inherited Metabolic Disease|September 16, 2003
CblE type of homocystinuria: mild clinical phenotype in two patients homozygous for a novel mutation in the MTRR geneM A Vilaseca, L Vilarinho, P Zavadakova, et al.
Journal of Inherited Metabolic Disease|October 17, 2006
Mutational spectrum of classical galactosaemia in Spain and PortugalL Gort, M D Boleda, L Tyfield, et al.
The Journal of Biological Chemistry|May 25, 1991
A 3-base pair in-frame deletion of the phenylalanine hydroxylase gene results in a kinetic variant of phenylketonuriaC Caillaud, S Lyonnet, F Rey, et al.
Human Genetics|April 1, 1992
Linkage disequilibrium between phenylketonuria and RFLP haplotype 1 at the phenylalanine hydroxylase locus in PortugalC Caillaud, L Vilarinho, A Vilarinho, et al.
Journal of the Neurological Sciences|June 17, 1999
The mitochondrial DNA A3243G mutation in Portugal: clinical and molecular studies in 5 familiesL Vilarinho, F M Santorelli, I Coelho, et al.
Pageof 5