Jove
Visualize
Contact Us
JoVE
x logofacebook logolinkedin logoyoutube logo
ABOUT JoVE
OverviewLeadershipBlogJoVE Help Center
AUTHORS
Publishing ProcessEditorial BoardScope & PoliciesPeer ReviewFAQSubmit
LIBRARIANS
TestimonialsSubscriptionsAccessResourcesLibrary Advisory BoardFAQ
RESEARCH
JoVE JournalMethods CollectionsJoVE Encyclopedia of ExperimentsArchive
EDUCATION
JoVE CoreJoVE BusinessJoVE Science EducationJoVE Lab ManualFaculty Resource CenterFaculty Site
Terms & Conditions of Use
Privacy Policy
Policies

Filters

Manuel Schiff

Showing results (61-70 of 159) with videos related to

Pageof 16
Sort By:
Neuromuscular Disorders : NMD|July 14, 2020
Evidence of diaphragmatic dysfunction with severe alveolar hypoventilation syndrome in mitochondrial respiratory chain deficiencyGiulia Barcia, Sonia Khirani, Alessandro Amaddeo, et al.
Journal of Inherited Metabolic Disease|December 10, 2019
Nocturnal enteral nutrition is therapeutic for growth failure in Fanconi-Bickel syndromeAlessandra Pennisi, Bruno Maranda, Jean-François Benoist, et al.
The Lancet. Diabetes & Endocrinology|May 23, 2021
Long-term safety and outcomes in hereditary tyrosinaemia type 1 with nitisinone treatment: a 15-year non-interventional, multicentre studyUte Spiekerkoetter, Maria L Couce, Anibh M Das, et al.
Orphanet Journal of Rare Diseases|September 25, 2016
Efficacy and safety of i.v. sodium benzoate in urea cycle disorders: a multicentre retrospective studyMarie-Caroline Husson, Manuel Schiff, Alain Fouilhoux, et al.
Pediatric Research|November 14, 2018
Wide clinical spectrum in ALG8-CDG: clues from molecular findings suggest an explanation for a milder phenotype in the first-described patientSandrine Vuillaumier-Barrot, Manuel Schiff, Francesca Mattioli, et al.
Orphanet Journal of Rare Diseases|October 31, 2019
Arabidopsis thaliana alternative dehydrogenases: a potential therapy for mitochondrial complex I deficiency? Perspectives and pitfallsAlessia Catania, Arcangela Iuso, Juliette Bouchereau, et al.
JIMD Reports|February 28, 2016
Abnormal Glycosylation Profile and High Alpha-Fetoprotein in a Patient with Twinkle VariantsJuliette Bouchereau, Sandrine Vuillaumier Barrot, Thierry Dupré, et al.
Kidney International Reports|December 19, 2024
Clinical Practice Recommendations on Kidney Management in Methylmalonic Acidemia: an Expert Consensus Statement From ERKNet and MetabERNAude Servais, Miriam Zacchia, Laurène Dehoux, et al.
Journal of Inherited Metabolic Disease|May 26, 2022
Very long-term outcomes in 23 patients with cblA type methylmalonic acidemiaCecilia Marelli, Alain Fouilhoux, Jean-Francois Benoist, et al.
Neuropediatrics|December 22, 2025
Hepatocellular Carcinoma: A Critical Complication in Patients Treated with Pyridoxal PhosphateMarion Brands, Chloe de Puyraimond, Sidney M Gospe, et al.
Pageof 16

Showing results (61-70 of 159) with videos related to

Sort By:
Pageof 16
Neuromuscular Disorders : NMD|July 14, 2020
Evidence of diaphragmatic dysfunction with severe alveolar hypoventilation syndrome in mitochondrial respiratory chain deficiencyGiulia Barcia, Sonia Khirani, Alessandro Amaddeo, et al.
Journal of Inherited Metabolic Disease|December 10, 2019
Nocturnal enteral nutrition is therapeutic for growth failure in Fanconi-Bickel syndromeAlessandra Pennisi, Bruno Maranda, Jean-François Benoist, et al.
The Lancet. Diabetes & Endocrinology|May 23, 2021
Long-term safety and outcomes in hereditary tyrosinaemia type 1 with nitisinone treatment: a 15-year non-interventional, multicentre studyUte Spiekerkoetter, Maria L Couce, Anibh M Das, et al.
Orphanet Journal of Rare Diseases|September 25, 2016
Efficacy and safety of i.v. sodium benzoate in urea cycle disorders: a multicentre retrospective studyMarie-Caroline Husson, Manuel Schiff, Alain Fouilhoux, et al.
Pediatric Research|November 14, 2018
Wide clinical spectrum in ALG8-CDG: clues from molecular findings suggest an explanation for a milder phenotype in the first-described patientSandrine Vuillaumier-Barrot, Manuel Schiff, Francesca Mattioli, et al.
Orphanet Journal of Rare Diseases|October 31, 2019
Arabidopsis thaliana alternative dehydrogenases: a potential therapy for mitochondrial complex I deficiency? Perspectives and pitfallsAlessia Catania, Arcangela Iuso, Juliette Bouchereau, et al.
JIMD Reports|February 28, 2016
Abnormal Glycosylation Profile and High Alpha-Fetoprotein in a Patient with Twinkle VariantsJuliette Bouchereau, Sandrine Vuillaumier Barrot, Thierry Dupré, et al.
Kidney International Reports|December 19, 2024
Clinical Practice Recommendations on Kidney Management in Methylmalonic Acidemia: an Expert Consensus Statement From ERKNet and MetabERNAude Servais, Miriam Zacchia, Laurène Dehoux, et al.
Journal of Inherited Metabolic Disease|May 26, 2022
Very long-term outcomes in 23 patients with cblA type methylmalonic acidemiaCecilia Marelli, Alain Fouilhoux, Jean-Francois Benoist, et al.
Neuropediatrics|December 22, 2025
Hepatocellular Carcinoma: A Critical Complication in Patients Treated with Pyridoxal PhosphateMarion Brands, Chloe de Puyraimond, Sidney M Gospe, et al.
Pageof 16