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Maria J Ferraz

Showing results (1-10 of 42) with videos related to

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Essays in Biochemistry|August 19, 2020
Lyso-glycosphingolipids: presence and consequencesMarco van Eijk, Maria J Ferraz, Rolf G Boot, et al.
Molecular Genetics and Metabolism|November 11, 2018
Dissociation of globotriaosylceramide and impaired endothelial function in α-galactosidase-A deficient EA.hy926 cellsNayiri Kaissarian, Justin Kang, Liming Shu, et al.
FEBS Letters|July 7, 2022
In situ glucosylceramide synthesis and its pharmacological inhibition analysed in cells by <sup>13</sup> C<sub>5</sub> -sphingosine precursor feeding and mass spectrometryRebecca E Katzy, Maria J Ferraz, Marc Hazeu, et al.
FEBS Letters|February 1, 2024
Mitochondrial dysfunction in NPC1-deficiency is not rescued by drugs targeting the glucosylceramidase GBA2 and the cholesterol-binding proteins TSPO and StARD1Simon Wheeler, Meenakshi Bhardwaj, Victor Kenyon, et al.
Orphanet Journal of Rare Diseases|March 25, 2016
Biochemical response to substrate reduction therapy versus enzyme replacement therapy in Gaucher disease type 1 patientsBouwien E Smid, Maria J Ferraz, Marri Verhoek, et al.
RSC Chemical Biology|February 12, 2025
Development of selective nanomolar cyclic peptide ligands as GBA1 enzyme stabilisersRebecca E Katzy, Renier H P van Neer, Maria J Ferraz, et al.
Journal of Lipid Research|April 30, 2013
Fetal asphyxia induces acute and persisting changes in the ceramide metabolism in rat brainEvi Vlassaks, Chiara Mencarelli, Maria Nikiforou, et al.
Chemical Communications (Cambridge, England)|September 25, 2024
Structure-guided design of C3-branched swainsonine as potent and selective human Golgi α-mannosidase (GMII) inhibitorTony Koemans, Megan Bennett, Maria J Ferraz, et al.
Clinica Chimica Acta; International Journal of Clinical Chemistry|September 18, 2020
Glucosylated cholesterol in skin: Synthetic role of extracellular glucocerebrosidaseDaphne E C Boer, Mina Mirzaian, Maria J Ferraz, et al.
Bioscience Reports|September 30, 2024
Favourable HDL composition in endurance athletes is not associated with changes in HDL in vitro antioxidant and endothelial anti-inflammatory functionJack David Beazer, Anne Sillars, Sally Beck, et al.
Pageof 5

Showing results (1-10 of 42) with videos related to

Sort By:
Pageof 5
Essays in Biochemistry|August 19, 2020
Lyso-glycosphingolipids: presence and consequencesMarco van Eijk, Maria J Ferraz, Rolf G Boot, et al.
Molecular Genetics and Metabolism|November 11, 2018
Dissociation of globotriaosylceramide and impaired endothelial function in α-galactosidase-A deficient EA.hy926 cellsNayiri Kaissarian, Justin Kang, Liming Shu, et al.
FEBS Letters|July 7, 2022
In situ glucosylceramide synthesis and its pharmacological inhibition analysed in cells by <sup>13</sup> C<sub>5</sub> -sphingosine precursor feeding and mass spectrometryRebecca E Katzy, Maria J Ferraz, Marc Hazeu, et al.
FEBS Letters|February 1, 2024
Mitochondrial dysfunction in NPC1-deficiency is not rescued by drugs targeting the glucosylceramidase GBA2 and the cholesterol-binding proteins TSPO and StARD1Simon Wheeler, Meenakshi Bhardwaj, Victor Kenyon, et al.
Orphanet Journal of Rare Diseases|March 25, 2016
Biochemical response to substrate reduction therapy versus enzyme replacement therapy in Gaucher disease type 1 patientsBouwien E Smid, Maria J Ferraz, Marri Verhoek, et al.
RSC Chemical Biology|February 12, 2025
Development of selective nanomolar cyclic peptide ligands as GBA1 enzyme stabilisersRebecca E Katzy, Renier H P van Neer, Maria J Ferraz, et al.
Journal of Lipid Research|April 30, 2013
Fetal asphyxia induces acute and persisting changes in the ceramide metabolism in rat brainEvi Vlassaks, Chiara Mencarelli, Maria Nikiforou, et al.
Chemical Communications (Cambridge, England)|September 25, 2024
Structure-guided design of C3-branched swainsonine as potent and selective human Golgi α-mannosidase (GMII) inhibitorTony Koemans, Megan Bennett, Maria J Ferraz, et al.
Clinica Chimica Acta; International Journal of Clinical Chemistry|September 18, 2020
Glucosylated cholesterol in skin: Synthetic role of extracellular glucocerebrosidaseDaphne E C Boer, Mina Mirzaian, Maria J Ferraz, et al.
Bioscience Reports|September 30, 2024
Favourable HDL composition in endurance athletes is not associated with changes in HDL in vitro antioxidant and endothelial anti-inflammatory functionJack David Beazer, Anne Sillars, Sally Beck, et al.
Pageof 5