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P G Pentchev

Showing results (41-50 of 120) with videos related to

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Acta Neuropathologica|January 1, 1987
Dysmyelination in NCTR-Balb/C mouse mutant with a lysosomal storage disorder. Morphological surveyH Weintraub, A Abramovici, U Sandbank, et al.
The Journal of Biological Chemistry|August 10, 1973
Isolation and characterization of glucocerebrosidase from human placental tissueP G Pentchev, R O Brady, S R Hibbert, et al.
Proceedings of the National Academy of Sciences of the United States of America|August 1, 1977
Enzyme replacement therapy in Gaucher's disease: large-scale purification of glucocerebrosidase suitable for human administrationF S Furbish, H E Blair, J Shiloach, et al.
Journal of Medical Genetics|October 1, 1978
A new form of Niemann-Pick disease characterised by temperature-labile sphingomyelinaseE L Schneider, P G Pentchev, S R Hibbert, et al.
Methods in Enzymology|January 1, 1975
Mutarotase (aldose 1-epimerase) from kidney cortexJ F Bailey, P H Fishman, J W Kusiak, et al.
The American Journal of Medicine|December 1, 1983
Normolipemic subcutaneous xanthomatosisR Fleischmajer, E J Schaefer, A E Gal, et al.
Pediatric Research|June 1, 1995
Cultured skin fibroblasts derived from patients with mucolipidosis 4 are auto-fluorescentE Goldin, E J Blanchette-Mackie, N K Dwyer, et al.
Analytical Biochemistry|May 1, 1979
The distribution of glucocerebroside in the liver of patients with Gaucher's diseaseA E Gal, P G Pentchev, J A Barranger, et al.
Biochimica Et Biophysica Acta|April 2, 1990
Abnormal cholesterol metabolism in imipramine-treated fibroblast cultures. Similarities with Niemann-Pick type C diseaseC Rodriguez-Lafrasse, R Rousson, J Bonnet, et al.
Proceedings of the National Academy of Sciences of the United States of America|August 1, 1978
Gaucher disease: isolation and comparison of normal and mutant glucocerebrosidase from human spleen tissueP G Pentchev, R O Brady, H E Blair, et al.
Pageof 12

Showing results (41-50 of 120) with videos related to

Sort By:
Pageof 12
Acta Neuropathologica|January 1, 1987
Dysmyelination in NCTR-Balb/C mouse mutant with a lysosomal storage disorder. Morphological surveyH Weintraub, A Abramovici, U Sandbank, et al.
The Journal of Biological Chemistry|August 10, 1973
Isolation and characterization of glucocerebrosidase from human placental tissueP G Pentchev, R O Brady, S R Hibbert, et al.
Proceedings of the National Academy of Sciences of the United States of America|August 1, 1977
Enzyme replacement therapy in Gaucher's disease: large-scale purification of glucocerebrosidase suitable for human administrationF S Furbish, H E Blair, J Shiloach, et al.
Journal of Medical Genetics|October 1, 1978
A new form of Niemann-Pick disease characterised by temperature-labile sphingomyelinaseE L Schneider, P G Pentchev, S R Hibbert, et al.
Methods in Enzymology|January 1, 1975
Mutarotase (aldose 1-epimerase) from kidney cortexJ F Bailey, P H Fishman, J W Kusiak, et al.
The American Journal of Medicine|December 1, 1983
Normolipemic subcutaneous xanthomatosisR Fleischmajer, E J Schaefer, A E Gal, et al.
Pediatric Research|June 1, 1995
Cultured skin fibroblasts derived from patients with mucolipidosis 4 are auto-fluorescentE Goldin, E J Blanchette-Mackie, N K Dwyer, et al.
Analytical Biochemistry|May 1, 1979
The distribution of glucocerebroside in the liver of patients with Gaucher's diseaseA E Gal, P G Pentchev, J A Barranger, et al.
Biochimica Et Biophysica Acta|April 2, 1990
Abnormal cholesterol metabolism in imipramine-treated fibroblast cultures. Similarities with Niemann-Pick type C diseaseC Rodriguez-Lafrasse, R Rousson, J Bonnet, et al.
Proceedings of the National Academy of Sciences of the United States of America|August 1, 1978
Gaucher disease: isolation and comparison of normal and mutant glucocerebrosidase from human spleen tissueP G Pentchev, R O Brady, H E Blair, et al.
Pageof 12