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P G Pentchev

Showing results (71-80 of 120) with videos related to

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Developmental Neuroscience|January 1, 1991
Type C Niemann-Pick disease: biochemical aspects and phenotypic heterogeneityM T Vanier, C Rodriguez-Lafrasse, R Rousson, et al.
American Journal of Medical Genetics|February 15, 1992
Niemann-Pick type-C disease: deficient intracellular transport of exogenously derived cholesterolC F Roff, E Goldin, M E Comly, et al.
Clinica Chimica Acta; International Journal of Clinical Chemistry|May 16, 1977
A practical chromogenic procedure for the diagnosis of Krabbe's diseaseA E Gal, R O Brady, P G Pentchev, et al.
The Journal of Biological Chemistry|December 15, 1986
Type C Niemann-Pick disease. A parallel loss of regulatory responses in both the uptake and esterification of low density lipoprotein-derived cholesterol in cultured fibroblastsP G Pentchev, H S Kruth, M E Comly, et al.
Journal of Biochemistry|June 5, 2001
Isolation of NPC1-deficient Chinese hamster ovary cell mutants by gene trap mutagenesisK Higaki, H Ninomiya, Y Sugimoto, et al.
Proceedings of the National Academy of Sciences of the United States of America|December 1, 1985
A defect in cholesterol esterification in Niemann-Pick disease (type C) patientsP G Pentchev, M E Comly, H S Kruth, et al.
Biochimica Et Biophysica Acta|June 5, 1991
Type C Niemann-Pick disease: spectrum of phenotypic variation in disruption of intracellular LDL-derived cholesterol processingM T Vanier, C Rodriguez-Lafrasse, R Rousson, et al.
Biochimica Et Biophysica Acta|August 19, 1992
Type C Niemann-Pick disease: a murine model of the lysosomal cholesterol lipidosis accumulates sphingosine and sphinganine in liverE Goldin, C F Roff, S P Miller, et al.
Proceedings of the National Academy of Sciences of the United States of America|January 1, 1979
Modification of the blood-brain barrier: increased concentration and fate of enzymes entering the brainJ A Barranger, S I Rapoport, W R Fredericks, et al.
Advances in Experimental Medicine and Biology|January 1, 1978
Factors that influence the uptake and turnover of glucocerebrosidase and alpha-galactosidase in mammalian liverP G Pentchev, J W Kusiak, J A Barranger, et al.
Pageof 12

Showing results (71-80 of 120) with videos related to

Sort By:
Pageof 12
Developmental Neuroscience|January 1, 1991
Type C Niemann-Pick disease: biochemical aspects and phenotypic heterogeneityM T Vanier, C Rodriguez-Lafrasse, R Rousson, et al.
American Journal of Medical Genetics|February 15, 1992
Niemann-Pick type-C disease: deficient intracellular transport of exogenously derived cholesterolC F Roff, E Goldin, M E Comly, et al.
Clinica Chimica Acta; International Journal of Clinical Chemistry|May 16, 1977
A practical chromogenic procedure for the diagnosis of Krabbe's diseaseA E Gal, R O Brady, P G Pentchev, et al.
The Journal of Biological Chemistry|December 15, 1986
Type C Niemann-Pick disease. A parallel loss of regulatory responses in both the uptake and esterification of low density lipoprotein-derived cholesterol in cultured fibroblastsP G Pentchev, H S Kruth, M E Comly, et al.
Journal of Biochemistry|June 5, 2001
Isolation of NPC1-deficient Chinese hamster ovary cell mutants by gene trap mutagenesisK Higaki, H Ninomiya, Y Sugimoto, et al.
Proceedings of the National Academy of Sciences of the United States of America|December 1, 1985
A defect in cholesterol esterification in Niemann-Pick disease (type C) patientsP G Pentchev, M E Comly, H S Kruth, et al.
Biochimica Et Biophysica Acta|June 5, 1991
Type C Niemann-Pick disease: spectrum of phenotypic variation in disruption of intracellular LDL-derived cholesterol processingM T Vanier, C Rodriguez-Lafrasse, R Rousson, et al.
Biochimica Et Biophysica Acta|August 19, 1992
Type C Niemann-Pick disease: a murine model of the lysosomal cholesterol lipidosis accumulates sphingosine and sphinganine in liverE Goldin, C F Roff, S P Miller, et al.
Proceedings of the National Academy of Sciences of the United States of America|January 1, 1979
Modification of the blood-brain barrier: increased concentration and fate of enzymes entering the brainJ A Barranger, S I Rapoport, W R Fredericks, et al.
Advances in Experimental Medicine and Biology|January 1, 1978
Factors that influence the uptake and turnover of glucocerebrosidase and alpha-galactosidase in mammalian liverP G Pentchev, J W Kusiak, J A Barranger, et al.
Pageof 12