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Paulo Gaspar

Showing results (11-20 of 28) with videos related to

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Human Molecular Genetics|April 22, 2008
A nonsense mutation in the LIMP-2 gene associated with progressive myoclonic epilepsy and nephrotic syndromeAndrea Balreira, Paulo Gaspar, Daniel Caiola, et al.
The FEBS Journal|December 24, 2014
Improving the accuracy of recombinant protein production through integration of bioinformatics, statistical and mass spectrometry methodologiesLapo Ragionieri, Rui Vitorino, Joerg Frommlet, et al.
Journal of Parkinson'S Disease|October 10, 2019
Parkinson's Disease and Fabry Disease: Clinical, Biochemical and Neuroimaging Analysis of Three PedigreesMiguel Fernandes Gago, Olga Azevedo, Andreia Guimarães, et al.
International Journal of Molecular Sciences|May 7, 2025
Establishment of a Human iPSC Line from Mucolipidosis Type II That Expresses the Key Markers of the DiseaseMaria Eduarda Moutinho, Mariana Gonçalves, Ana Joana Duarte, et al.
International Journal of Molecular Sciences|February 13, 2025
mRNA Degradation as a Therapeutic Solution for Mucopolysaccharidosis Type IIIC: Use of Antisense Oligonucleotides to Promote Downregulation of Heparan Sulfate SynthesisJuliana Inês Santos, Mariana Gonçalves, Matilde Barbosa Almeida, et al.
Journal of Lipid Research|November 12, 2013
Action myoclonus-renal failure syndrome: diagnostic applications of activity-based probes and lipid analysisPaulo Gaspar, Wouter W Kallemeijn, Anneke Strijland, et al.
Proceedings of the National Academy of Sciences of the United States of America|October 16, 2014
LIMP-2 expression is critical for β-glucocerebrosidase activity and α-synuclein clearanceMichelle Rothaug, Friederike Zunke, Joseph R Mazzulli, et al.
Molecular Genetics and Metabolism|January 12, 2016
Lyso-glycosphingolipid abnormalities in different murine models of lysosomal storage disordersMaria J Ferraz, André R A Marques, Paulo Gaspar, et al.
Orphanet Journal of Rare Diseases|June 18, 2026
Relevance of functional studies for assessing an antisense oligonucleotide-mediated exon skipping therapeutic strategy for mucolipidosis type IIMariana Gonçalves, Marisa Encarnação, Luciana Moreira, et al.
Molecular Genetics and Metabolism|September 15, 2019
Founder effect of Fabry disease due to p.F113L mutation: Clinical profile of a late-onset phenotypeOlga Azevedo, Andreas Gal, Rui Faria, et al.
Pageof 3

Showing results (11-20 of 28) with videos related to

Sort By:
Pageof 3
Human Molecular Genetics|April 22, 2008
A nonsense mutation in the LIMP-2 gene associated with progressive myoclonic epilepsy and nephrotic syndromeAndrea Balreira, Paulo Gaspar, Daniel Caiola, et al.
The FEBS Journal|December 24, 2014
Improving the accuracy of recombinant protein production through integration of bioinformatics, statistical and mass spectrometry methodologiesLapo Ragionieri, Rui Vitorino, Joerg Frommlet, et al.
Journal of Parkinson'S Disease|October 10, 2019
Parkinson's Disease and Fabry Disease: Clinical, Biochemical and Neuroimaging Analysis of Three PedigreesMiguel Fernandes Gago, Olga Azevedo, Andreia Guimarães, et al.
International Journal of Molecular Sciences|May 7, 2025
Establishment of a Human iPSC Line from Mucolipidosis Type II That Expresses the Key Markers of the DiseaseMaria Eduarda Moutinho, Mariana Gonçalves, Ana Joana Duarte, et al.
International Journal of Molecular Sciences|February 13, 2025
mRNA Degradation as a Therapeutic Solution for Mucopolysaccharidosis Type IIIC: Use of Antisense Oligonucleotides to Promote Downregulation of Heparan Sulfate SynthesisJuliana Inês Santos, Mariana Gonçalves, Matilde Barbosa Almeida, et al.
Journal of Lipid Research|November 12, 2013
Action myoclonus-renal failure syndrome: diagnostic applications of activity-based probes and lipid analysisPaulo Gaspar, Wouter W Kallemeijn, Anneke Strijland, et al.
Proceedings of the National Academy of Sciences of the United States of America|October 16, 2014
LIMP-2 expression is critical for β-glucocerebrosidase activity and α-synuclein clearanceMichelle Rothaug, Friederike Zunke, Joseph R Mazzulli, et al.
Molecular Genetics and Metabolism|January 12, 2016
Lyso-glycosphingolipid abnormalities in different murine models of lysosomal storage disordersMaria J Ferraz, André R A Marques, Paulo Gaspar, et al.
Orphanet Journal of Rare Diseases|June 18, 2026
Relevance of functional studies for assessing an antisense oligonucleotide-mediated exon skipping therapeutic strategy for mucolipidosis type IIMariana Gonçalves, Marisa Encarnação, Luciana Moreira, et al.
Molecular Genetics and Metabolism|September 15, 2019
Founder effect of Fabry disease due to p.F113L mutation: Clinical profile of a late-onset phenotypeOlga Azevedo, Andreas Gal, Rui Faria, et al.
Pageof 3