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The Biochemical Journal|June 24, 2008
Dipeptidyl-peptidase I does not functionally compensate for the loss of tripeptidyl-peptidase I in the neurodegenerative disease late-infantile neuronal ceroid lipofuscinosisKwi-Hye Kim, Christine T Pham, David E Sleat, et al.
The Journal of Biological Chemistry|April 12, 2006
Mechanism of cholesterol transfer from the Niemann-Pick type C2 protein to model membranes supports a role in lysosomal cholesterol transportSunita R Cheruku, Zhi Xu, Roxanne Dutia, et al.
Plos One|March 4, 2014
Potential pitfalls and solutions for use of fluorescent fusion proteins to study the lysosomeLing Huang, Douglas Pike, David E Sleat, et al.
Plos One|July 14, 2012
Systemic administration of tripeptidyl peptidase I in a mouse model of late infantile neuronal ceroid lipofuscinosis: effect of glycan modificationYu Meng, Istvan Sohar, Lingling Wang, et al.
Gene|August 25, 2016
Analysis of large-scale whole exome sequencing data to determine the prevalence of genetically-distinct forms of neuronal ceroid lipofuscinosisDavid E Sleat, Erika Gedvilaite, Yeting Zhang, et al.
Molecular & Cellular Proteomics : MCP|September 13, 2007
Proteomics analysis of serum from mutant mice reveals lysosomal proteins selectively transported by each of the two mannose 6-phosphate receptorsMeiqian Qian, David E Sleat, Haiyan Zheng, et al.
The Journal of Biological Chemistry|November 29, 2008
Crystal structure and autoactivation pathway of the precursor form of human tripeptidyl-peptidase 1, the enzyme deficient in late infantile ceroid lipofuscinosisJayita Guhaniyogi, Istvan Sohar, Kalyan Das, et al.
The Journal of Biological Chemistry|June 19, 2007
Structural basis of sterol binding by NPC2, a lysosomal protein deficient in Niemann-Pick type C2 diseaseSujuan Xu, Brian Benoff, Heng-Ling Liou, et al.
Plos One|February 7, 2018
Inducible transgenic expression of tripeptidyl peptidase 1 in a mouse model of late-infantile neuronal ceroid lipofuscinosisYuliya Nemtsova, Jennifer A Wiseman, Mukarram El-Banna, et al.
Molecular Therapy : the Journal of the American Society of Gene Therapy|July 7, 2011
Large-volume intrathecal enzyme delivery increases survival of a mouse model of late infantile neuronal ceroid lipofuscinosisSu Xu, Lingling Wang, Mukarram El-Banna, et al.
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