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Pierre Rustin

Showing results (11-20 of 154) with videos related to

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The Journal of Biological Chemistry|September 21, 2011
Mutations in the dimer interface of dihydrolipoamide dehydrogenase promote site-specific oxidative damages in yeast and human cellsRachael A Vaubel, Pierre Rustin, Grazia Isaya
Free Radical Research|June 19, 2002
Coenzyme Q10 depletion is comparatively less detrimental to human cultured skin fibroblasts than respiratory chain complex deficienciesVanna Geromel, Agnès Rötig, Arnold Munnich, et al.
Free Radical Research|June 19, 2002
Heart hypertrophy and function are improved by idebenone in Friedreich's ataxiaPierre Rustin, Agnès Rötig, Arnold Munnich, et al.
Trends in Molecular Medicine|June 18, 2002
Molecular insights into Friedreich's ataxia and antioxidant-based therapiesAgnès Rötig, Daniel Sidi, Arnold Munnich, et al.
Biochemical and Biophysical Research Communications|March 27, 2004
Quinone analogues regulate mitochondrial substrate competitive oxidationJean-Jacques Brière, Dimitri Schlemmer, Domique Chretien, et al.
Biochimica Et Biophysica Acta|December 4, 2004
Respiratory chain defects: what do we know for sure about their consequences in vivo?Jean-Jacques Brière, Dominique Chrétien, Paule Bénit, et al.
BMC Neurology|June 19, 2008
Deferiprone targets aconitase: implication for Friedreich's ataxia treatmentSergio Goncalves, Vincent Paupe, Emmanuel P Dassa, et al.
Trends in Biochemical Sciences|April 1, 2025
Mitochondrial heat production: the elephant in the lab…Pierre Rustin, Howard T Jacobs, Mügen Terzioglu, et al.
BMC Medicine|October 12, 2011
Friedreich's ataxia: the vicious circle hypothesis revisitedAurélien Bayot, Renata Santos, Jean-Michel Camadro, et al.
Bulletin De L'Academie Nationale De Medecine|September 2, 2009
[Mitochondrial disorders]Arnold Munnich, Pascale de Lonlay, Agnès Rötig, et al.
Pageof 16

Showing results (11-20 of 154) with videos related to

Sort By:
Pageof 16
The Journal of Biological Chemistry|September 21, 2011
Mutations in the dimer interface of dihydrolipoamide dehydrogenase promote site-specific oxidative damages in yeast and human cellsRachael A Vaubel, Pierre Rustin, Grazia Isaya
Free Radical Research|June 19, 2002
Coenzyme Q10 depletion is comparatively less detrimental to human cultured skin fibroblasts than respiratory chain complex deficienciesVanna Geromel, Agnès Rötig, Arnold Munnich, et al.
Free Radical Research|June 19, 2002
Heart hypertrophy and function are improved by idebenone in Friedreich's ataxiaPierre Rustin, Agnès Rötig, Arnold Munnich, et al.
Trends in Molecular Medicine|June 18, 2002
Molecular insights into Friedreich's ataxia and antioxidant-based therapiesAgnès Rötig, Daniel Sidi, Arnold Munnich, et al.
Biochemical and Biophysical Research Communications|March 27, 2004
Quinone analogues regulate mitochondrial substrate competitive oxidationJean-Jacques Brière, Dimitri Schlemmer, Domique Chretien, et al.
Biochimica Et Biophysica Acta|December 4, 2004
Respiratory chain defects: what do we know for sure about their consequences in vivo?Jean-Jacques Brière, Dominique Chrétien, Paule Bénit, et al.
BMC Neurology|June 19, 2008
Deferiprone targets aconitase: implication for Friedreich's ataxia treatmentSergio Goncalves, Vincent Paupe, Emmanuel P Dassa, et al.
Trends in Biochemical Sciences|April 1, 2025
Mitochondrial heat production: the elephant in the lab…Pierre Rustin, Howard T Jacobs, Mügen Terzioglu, et al.
BMC Medicine|October 12, 2011
Friedreich's ataxia: the vicious circle hypothesis revisitedAurélien Bayot, Renata Santos, Jean-Michel Camadro, et al.
Bulletin De L'Academie Nationale De Medecine|September 2, 2009
[Mitochondrial disorders]Arnold Munnich, Pascale de Lonlay, Agnès Rötig, et al.
Pageof 16