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R D Steiner

Showing results (31-40 of 41) with videos related to

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Neurology|March 12, 2003
Remarkable improvement in adult Leigh syndrome with partial cytochrome c oxidase deficiencyP C Goldenberg, R D Steiner, L S Merkens, et al.
American Journal of Medical Genetics|September 20, 2000
Mutation analysis and description of sixteen RSH/Smith-Lemli-Opitz syndrome patients: polymerase chain reaction-based assays to simplify genotypingP A Krakowiak, N A Nwokoro, C A Wassif, et al.
Journal of Inherited Metabolic Disease|November 17, 2007
Deletion of a single mevalonate kinase (Mvk) allele yields a murine model of hyper-IgD syndromeE J Hager, H M Tse, J D Piganelli, et al.
Human Molecular Genetics|March 7, 2001
Biochemical, phenotypic and neurophysiological characterization of a genetic mouse model of RSH/Smith--Lemli--Opitz syndromeC A Wassif, P Zhu, L Kratz, et al.
Prenatal Diagnosis|March 17, 2000
Fetal demise with Smith-Lemli-Opitz syndrome confirmed by tissue sterol analysis and the absence of measurable 7-dehydrocholesterol Delta(7)-reductase activity in chorionic villiL M Linck, S J Hayflick, D S Lin, et al.
Journal of Medical Genetics|April 5, 2005
DHCR7 nonsense mutations and characterisation of mRNA nonsense mediated decay in Smith-Lemli-Opitz syndromeL S Correa-Cerro, C A Wassif, J S Waye, et al.
Pediatric Research|June 1, 2000
2-Methylbutyryl-coenzyme A dehydrogenase deficiency: a new inborn error of L-isoleucine metabolismK M Gibson, T G Burlingame, B Hogema, et al.
Clinical Genetics|April 24, 2014
A cross-sectional multicenter study of osteogenesis imperfecta in North America - results from the linked clinical research centersR M Patel, S C S Nagamani, D Cuthbertson, et al.
Genetics in Medicine : Official Journal of the American College of Medical Genetics|October 2, 2015
Cesarean delivery is not associated with decreased at-birth fracture rates in osteogenesis imperfectaS Bellur, M Jain, D Cuthbertson, et al.
The Journal of Clinical Endocrinology and Metabolism|November 26, 2010
Alendronate for the treatment of pediatric osteogenesis imperfecta: a randomized placebo-controlled studyL M Ward, F Rauch, M P Whyte, et al.
Pageof 5

Showing results (31-40 of 41) with videos related to

Sort By:
Pageof 5
Neurology|March 12, 2003
Remarkable improvement in adult Leigh syndrome with partial cytochrome c oxidase deficiencyP C Goldenberg, R D Steiner, L S Merkens, et al.
American Journal of Medical Genetics|September 20, 2000
Mutation analysis and description of sixteen RSH/Smith-Lemli-Opitz syndrome patients: polymerase chain reaction-based assays to simplify genotypingP A Krakowiak, N A Nwokoro, C A Wassif, et al.
Journal of Inherited Metabolic Disease|November 17, 2007
Deletion of a single mevalonate kinase (Mvk) allele yields a murine model of hyper-IgD syndromeE J Hager, H M Tse, J D Piganelli, et al.
Human Molecular Genetics|March 7, 2001
Biochemical, phenotypic and neurophysiological characterization of a genetic mouse model of RSH/Smith--Lemli--Opitz syndromeC A Wassif, P Zhu, L Kratz, et al.
Prenatal Diagnosis|March 17, 2000
Fetal demise with Smith-Lemli-Opitz syndrome confirmed by tissue sterol analysis and the absence of measurable 7-dehydrocholesterol Delta(7)-reductase activity in chorionic villiL M Linck, S J Hayflick, D S Lin, et al.
Journal of Medical Genetics|April 5, 2005
DHCR7 nonsense mutations and characterisation of mRNA nonsense mediated decay in Smith-Lemli-Opitz syndromeL S Correa-Cerro, C A Wassif, J S Waye, et al.
Pediatric Research|June 1, 2000
2-Methylbutyryl-coenzyme A dehydrogenase deficiency: a new inborn error of L-isoleucine metabolismK M Gibson, T G Burlingame, B Hogema, et al.
Clinical Genetics|April 24, 2014
A cross-sectional multicenter study of osteogenesis imperfecta in North America - results from the linked clinical research centersR M Patel, S C S Nagamani, D Cuthbertson, et al.
Genetics in Medicine : Official Journal of the American College of Medical Genetics|October 2, 2015
Cesarean delivery is not associated with decreased at-birth fracture rates in osteogenesis imperfectaS Bellur, M Jain, D Cuthbertson, et al.
The Journal of Clinical Endocrinology and Metabolism|November 26, 2010
Alendronate for the treatment of pediatric osteogenesis imperfecta: a randomized placebo-controlled studyL M Ward, F Rauch, M P Whyte, et al.
Pageof 5