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Raphael Schiffmann

Showing results (171-180 of 225) with videos related to

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Journal of Neuroinflammation|December 30, 2019
Unique molecular signature in mucolipidosis type IV microgliaAntony Cougnoux, Rebecca A Drummond, Mason Fellmeth, et al.
Genetics in Medicine : Official Journal of the American College of Medical Genetics|May 18, 2013
Changes in plasma and urine globotriaosylceramide levels do not predict Fabry disease progression over 1 year of agalsidase alfaRaphael Schiffmann, Markus Ries, Derek Blankenship, et al.
Journal of the American Heart Association|February 6, 2014
Risk of death in heart disease is associated with elevated urinary globotriaosylceramideRaphael Schiffmann, Sabrina Forni, Caren Swift, et al.
Journal of Neurology, Neurosurgery, and Psychiatry|November 6, 2015
Triheptanoin dramatically reduces paroxysmal motor disorder in patients with GLUT1 deficiencyFanny Mochel, Elodie Hainque, Domitille Gras, et al.
Pediatrics|February 17, 2005
Pediatric Fabry diseaseMarkus Ries, Surya Gupta, David F Moore, et al.
DNA Repair|October 29, 2008
XPC initiation codon mutation in xeroderma pigmentosum patients with and without neurological symptomsSikandar G Khan, Kyu-Seon Oh, Steffen Emmert, et al.
Human Molecular Genetics|October 4, 2017
TUBB4A mutations result in specific neuronal and oligodendrocytic defects that closely match clinically distinct phenotypesJulian Curiel, Guillermo Rodríguez Bey, Asako Takanohashi, et al.
Human Molecular Genetics|February 4, 2017
Tetrahydrobiopterin deficiency in the pathogenesis of Fabry diseaseJin-Song Shen, Erland Arning, Michael L West, et al.
CNS Neuroscience & Therapeutics|February 15, 2024
GDF15 is a dynamic biomarker of the integrated stress response in the central nervous systemJyoti Asundi, Chunlian Zhang, Diana Donnelly-Roberts, et al.
Molecular Genetics and Metabolism|May 20, 2026
Diagnostic and therapeutic applications of the glycan biomarker H3N2b in GM1 GangliosidosisPamela Kell, Sonali Mishra, Precilla D'Souza, et al.
Pageof 23

Showing results (171-180 of 225) with videos related to

Sort By:
Pageof 23
Journal of Neuroinflammation|December 30, 2019
Unique molecular signature in mucolipidosis type IV microgliaAntony Cougnoux, Rebecca A Drummond, Mason Fellmeth, et al.
Genetics in Medicine : Official Journal of the American College of Medical Genetics|May 18, 2013
Changes in plasma and urine globotriaosylceramide levels do not predict Fabry disease progression over 1 year of agalsidase alfaRaphael Schiffmann, Markus Ries, Derek Blankenship, et al.
Journal of the American Heart Association|February 6, 2014
Risk of death in heart disease is associated with elevated urinary globotriaosylceramideRaphael Schiffmann, Sabrina Forni, Caren Swift, et al.
Journal of Neurology, Neurosurgery, and Psychiatry|November 6, 2015
Triheptanoin dramatically reduces paroxysmal motor disorder in patients with GLUT1 deficiencyFanny Mochel, Elodie Hainque, Domitille Gras, et al.
Pediatrics|February 17, 2005
Pediatric Fabry diseaseMarkus Ries, Surya Gupta, David F Moore, et al.
DNA Repair|October 29, 2008
XPC initiation codon mutation in xeroderma pigmentosum patients with and without neurological symptomsSikandar G Khan, Kyu-Seon Oh, Steffen Emmert, et al.
Human Molecular Genetics|October 4, 2017
TUBB4A mutations result in specific neuronal and oligodendrocytic defects that closely match clinically distinct phenotypesJulian Curiel, Guillermo Rodríguez Bey, Asako Takanohashi, et al.
Human Molecular Genetics|February 4, 2017
Tetrahydrobiopterin deficiency in the pathogenesis of Fabry diseaseJin-Song Shen, Erland Arning, Michael L West, et al.
CNS Neuroscience & Therapeutics|February 15, 2024
GDF15 is a dynamic biomarker of the integrated stress response in the central nervous systemJyoti Asundi, Chunlian Zhang, Diana Donnelly-Roberts, et al.
Molecular Genetics and Metabolism|May 20, 2026
Diagnostic and therapeutic applications of the glycan biomarker H3N2b in GM1 GangliosidosisPamela Kell, Sonali Mishra, Precilla D'Souza, et al.
Pageof 23