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Raphael Schiffmann

Showing results (181-190 of 225) with videos related to

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JAMA Neurology|February 10, 2015
Deep intronic GBE1 mutation in manifesting heterozygous patients with adult polyglucosan body diseaseH Orhan Akman, Or Kakhlon, Jorida Coku, et al.
Annals of Neurology|December 19, 2003
Insertion of mutant proteolipid protein results in missorting of myelin proteinsCatherine Vaurs-Barriere, Kondi Wong, Thais D Weibel, et al.
Brain : a Journal of Neurology|February 1, 2013
Auditory analysis of xeroderma pigmentosum 1971-2012: hearing function, sun sensitivity and DNA repair predict neurological degenerationMariam B Totonchy, Deborah Tamura, Matthew S Pantell, et al.
American Journal of Human Genetics|August 23, 2011
Mutations of POLR3A encoding a catalytic subunit of RNA polymerase Pol III cause a recessive hypomyelinating leukodystrophyGeneviève Bernard, Eliane Chouery, Maria Lisa Putorti, et al.
Orphanet Journal of Rare Diseases|April 29, 2018
Migalastat improves diarrhea in patients with Fabry disease: clinical-biomarker correlations from the phase 3 FACETS trialRaphael Schiffmann, Daniel G Bichet, Ana Jovanovic, et al.
The FEBS Journal|February 13, 2010
The pharmacological chaperone isofagomine increases the activity of the Gaucher disease L444P mutant form of beta-glucosidaseRichie Khanna, Elfrida R Benjamin, Lee Pellegrino, et al.
Brain : a Journal of Neurology|May 3, 2014
Hypomyelination with atrophy of the basal ganglia and cerebellum: further delineation of the phenotype and genotype-phenotype correlationEline M Hamilton, Emiel Polder, Adeline Vanderver, et al.
Nature Communications|May 2, 2019
The glycosylation design space for recombinant lysosomal replacement enzymes produced in CHO cellsWeihua Tian, Zilu Ye, Shengjun Wang, et al.
Neurology. Genetics|February 7, 2022
Therapy Trial Design in Vanishing White Matter: An Expert Consortium OpinionMarjo S van der Knaap, Joshua L Bonkowsky, Adeline Vanderver, et al.
Annals of Neurology|June 27, 2009
Free sialic acid storage disease without sialuriaFanny Mochel, Bingzhi Yang, Julie Barritault, et al.
Pageof 23

Showing results (181-190 of 225) with videos related to

Sort By:
Pageof 23
JAMA Neurology|February 10, 2015
Deep intronic GBE1 mutation in manifesting heterozygous patients with adult polyglucosan body diseaseH Orhan Akman, Or Kakhlon, Jorida Coku, et al.
Annals of Neurology|December 19, 2003
Insertion of mutant proteolipid protein results in missorting of myelin proteinsCatherine Vaurs-Barriere, Kondi Wong, Thais D Weibel, et al.
Brain : a Journal of Neurology|February 1, 2013
Auditory analysis of xeroderma pigmentosum 1971-2012: hearing function, sun sensitivity and DNA repair predict neurological degenerationMariam B Totonchy, Deborah Tamura, Matthew S Pantell, et al.
American Journal of Human Genetics|August 23, 2011
Mutations of POLR3A encoding a catalytic subunit of RNA polymerase Pol III cause a recessive hypomyelinating leukodystrophyGeneviève Bernard, Eliane Chouery, Maria Lisa Putorti, et al.
Orphanet Journal of Rare Diseases|April 29, 2018
Migalastat improves diarrhea in patients with Fabry disease: clinical-biomarker correlations from the phase 3 FACETS trialRaphael Schiffmann, Daniel G Bichet, Ana Jovanovic, et al.
The FEBS Journal|February 13, 2010
The pharmacological chaperone isofagomine increases the activity of the Gaucher disease L444P mutant form of beta-glucosidaseRichie Khanna, Elfrida R Benjamin, Lee Pellegrino, et al.
Brain : a Journal of Neurology|May 3, 2014
Hypomyelination with atrophy of the basal ganglia and cerebellum: further delineation of the phenotype and genotype-phenotype correlationEline M Hamilton, Emiel Polder, Adeline Vanderver, et al.
Nature Communications|May 2, 2019
The glycosylation design space for recombinant lysosomal replacement enzymes produced in CHO cellsWeihua Tian, Zilu Ye, Shengjun Wang, et al.
Neurology. Genetics|February 7, 2022
Therapy Trial Design in Vanishing White Matter: An Expert Consortium OpinionMarjo S van der Knaap, Joshua L Bonkowsky, Adeline Vanderver, et al.
Annals of Neurology|June 27, 2009
Free sialic acid storage disease without sialuriaFanny Mochel, Bingzhi Yang, Julie Barritault, et al.
Pageof 23