Jove
Visualize
Contact Us
JoVE
x logofacebook logolinkedin logoyoutube logo
ABOUT JoVE
OverviewLeadershipBlogJoVE Help Center
AUTHORS
Publishing ProcessEditorial BoardScope & PoliciesPeer ReviewFAQSubmit
LIBRARIANS
TestimonialsSubscriptionsAccessResourcesLibrary Advisory BoardFAQ
RESEARCH
JoVE JournalMethods CollectionsJoVE Encyclopedia of ExperimentsArchive
EDUCATION
JoVE CoreJoVE BusinessJoVE Science EducationJoVE Lab ManualFaculty Resource CenterFaculty Site
Terms & Conditions of Use
Privacy Policy
Policies

Filters

Richard J Rodenburg

Showing results (41-50 of 137) with videos related to

Pageof 14
Sort By:
European Journal of Human Genetics : EJHG|December 15, 2010
NDUFA10 mutations cause complex I deficiency in a patient with Leigh diseaseSaskia J G Hoefs, Francjan J van Spronsen, Ellen W H Lenssen, et al.
European Journal of Human Genetics : EJHG|December 2, 2010
Mutation in subdomain G' of mitochondrial elongation factor G1 is associated with combined OXPHOS deficiency in fibroblasts but not in musclePaulien Smits, Hana Antonicka, Peter M van Hasselt, et al.
Biochimica Et Biophysica Acta|February 18, 2015
Skeletal muscle mitochondria of NDUFS4-/- mice display normal maximal pyruvate oxidation and ATP productionMohammad T Alam, Ganesh R Manjeri, Richard J Rodenburg, et al.
Metabolomics : Official Journal of the Metabolomic Society|January 13, 2021
One mutation, three phenotypes: novel metabolic insights on MELAS, MIDD and myopathy caused by the m.3243A > G mutationKarien Esterhuizen, J Zander Lindeque, Shayne Mason, et al.
Genes|May 25, 2024
Mutations in <i>NSUN3</i>, a Mitochondrial Methyl Transferase Gene, Cause Inherited Optic NeuropathyCansu de Muijnck, Jacoline B Ten Brink, Hugoline G de Haan, et al.
Molecular Genetics and Metabolism|March 27, 2007
Investigation of the complex I assembly chaperones B17.2L and NDUFAF1 in a cohort of CI deficient patientsRutger O Vogel, Mariël A M van den Brand, Richard J Rodenburg, et al.
Human Mutation|March 11, 2015
Novel, compound heterozygous, single-nucleotide variants in MARS2 associated with developmental delay, poor growth, and sensorineural hearing lossBryn D Webb, Patricia G Wheeler, Jacob J Hagen, et al.
Journal of the American College of Cardiology|November 19, 2021
Moderate Intensity Exercise Training Improves Skeletal Muscle Performance in Symptomatic and Asymptomatic Statin UsersNeeltje A E Allard, Lando Janssen, Thorben Aussieker, et al.
Plos Computational Biology|August 7, 2023
Comparative Clustering (CompaCt) of eukaryote complexomes identifies novel interactions and sheds light on protein complex evolutionJoeri van Strien, Felix Evers, Madhurya Lutikurti, et al.
JIMD Reports|January 4, 2016
Atypical Clinical Presentations of TAZ Mutations: An Underdiagnosed Cause of Growth Retardation?Charlotte Thiels, Martin Fleger, Martina Huemer, et al.
Pageof 14

Showing results (41-50 of 137) with videos related to

Sort By:
Pageof 14
European Journal of Human Genetics : EJHG|December 15, 2010
NDUFA10 mutations cause complex I deficiency in a patient with Leigh diseaseSaskia J G Hoefs, Francjan J van Spronsen, Ellen W H Lenssen, et al.
European Journal of Human Genetics : EJHG|December 2, 2010
Mutation in subdomain G' of mitochondrial elongation factor G1 is associated with combined OXPHOS deficiency in fibroblasts but not in musclePaulien Smits, Hana Antonicka, Peter M van Hasselt, et al.
Biochimica Et Biophysica Acta|February 18, 2015
Skeletal muscle mitochondria of NDUFS4-/- mice display normal maximal pyruvate oxidation and ATP productionMohammad T Alam, Ganesh R Manjeri, Richard J Rodenburg, et al.
Metabolomics : Official Journal of the Metabolomic Society|January 13, 2021
One mutation, three phenotypes: novel metabolic insights on MELAS, MIDD and myopathy caused by the m.3243A > G mutationKarien Esterhuizen, J Zander Lindeque, Shayne Mason, et al.
Genes|May 25, 2024
Mutations in <i>NSUN3</i>, a Mitochondrial Methyl Transferase Gene, Cause Inherited Optic NeuropathyCansu de Muijnck, Jacoline B Ten Brink, Hugoline G de Haan, et al.
Molecular Genetics and Metabolism|March 27, 2007
Investigation of the complex I assembly chaperones B17.2L and NDUFAF1 in a cohort of CI deficient patientsRutger O Vogel, Mariël A M van den Brand, Richard J Rodenburg, et al.
Human Mutation|March 11, 2015
Novel, compound heterozygous, single-nucleotide variants in MARS2 associated with developmental delay, poor growth, and sensorineural hearing lossBryn D Webb, Patricia G Wheeler, Jacob J Hagen, et al.
Journal of the American College of Cardiology|November 19, 2021
Moderate Intensity Exercise Training Improves Skeletal Muscle Performance in Symptomatic and Asymptomatic Statin UsersNeeltje A E Allard, Lando Janssen, Thorben Aussieker, et al.
Plos Computational Biology|August 7, 2023
Comparative Clustering (CompaCt) of eukaryote complexomes identifies novel interactions and sheds light on protein complex evolutionJoeri van Strien, Felix Evers, Madhurya Lutikurti, et al.
JIMD Reports|January 4, 2016
Atypical Clinical Presentations of TAZ Mutations: An Underdiagnosed Cause of Growth Retardation?Charlotte Thiels, Martin Fleger, Martina Huemer, et al.
Pageof 14