Jove
Visualize
Contact Us
JoVE
x logofacebook logolinkedin logoyoutube logo
ABOUT JoVE
OverviewLeadershipBlogJoVE Help Center
AUTHORS
Publishing ProcessEditorial BoardScope & PoliciesPeer ReviewFAQSubmit
LIBRARIANS
TestimonialsSubscriptionsAccessResourcesLibrary Advisory BoardFAQ
RESEARCH
JoVE JournalMethods CollectionsJoVE Encyclopedia of ExperimentsArchive
EDUCATION
JoVE CoreJoVE BusinessJoVE Science EducationJoVE Lab ManualFaculty Resource CenterFaculty Site
Terms & Conditions of Use
Privacy Policy
Policies

Filters

Sara Boenzi

Showing results (1-10 of 44) with videos related to

Pageof 5
Sort By:
Essays in Biochemistry|July 8, 2018
Biomarkers for mitochondrial energy metabolism diseasesSara Boenzi, Daria Diodato
American Journal of Medical Genetics. Part C, Seminars in Medical Genetics|April 8, 2006
Methylmalonic and propionic aciduriaFederica Deodato, Sara Boenzi, Filippo M Santorelli, et al.
BMJ Case Reports|May 4, 2026
β-ureidopropionase deficiency mimicking Leigh syndrome associated with methylmalonic aciduriaGiulia Ferrera, Sara Boenzi, Eleonora Lamantea, et al.
Molecular Genetics and Metabolism|June 15, 2013
Optimizing the dose of hydroxocobalamin in cobalamin C (cblC) defectCarlo Dionisi-Vici, Diego Martinelli, Ferdinando Ceravolo, et al.
Frontiers in Pediatrics|January 21, 2025
Case Report: Two years of compassionate use with Olipudase-alfa in a child with neurovisceral acid sphingomyelinase deficiencyFederica Deodato, Sara Boenzi, Benedetta Greco, et al.
Molecular Genetics and Metabolism|November 23, 2021
Comprehensive-targeted lipidomic analysis in Niemann-Pick C diseaseSara Boenzi, Giulio Catesini, Elisa Sacchetti, et al.
Journal of Lipid Research|January 7, 2016
Evaluation of plasma cholestane-3β,5α,6β-triol and 7-ketocholesterol in inherited disorders related to cholesterol metabolismSara Boenzi, Federica Deodato, Roberta Taurisano, et al.
Ophthalmology|August 5, 2009
Retinal degenerationChiara Morini, Paolo Capozzi, Sara Boenzi, et al.
Journal of Lipid Research|December 22, 2025
New Multiplex LC-MS/MS Method for lipid biomarker Analysis of Inherited Neurodegenerative Metabolic DiseasesAnna Sidorina, Giulio Catesini, Federica Deodato, et al.
Clinica Chimica Acta; International Journal of Clinical Chemistry|May 19, 2016
A new multiplex method for the diagnosis of peroxisomal disorders allowing simultaneous determination of plasma very-long-chain fatty acids, phytanic, pristanic, docosahexaenoic and bile acids by high-performance liquid chromatography-atmospheric pressure chemical ionization-tandem mass spectrometryMichela Semeraro, Cristiano Rizzo, Sara Boenzi, et al.
Pageof 5

Showing results (1-10 of 44) with videos related to

Sort By:
Pageof 5
Essays in Biochemistry|July 8, 2018
Biomarkers for mitochondrial energy metabolism diseasesSara Boenzi, Daria Diodato
American Journal of Medical Genetics. Part C, Seminars in Medical Genetics|April 8, 2006
Methylmalonic and propionic aciduriaFederica Deodato, Sara Boenzi, Filippo M Santorelli, et al.
BMJ Case Reports|May 4, 2026
β-ureidopropionase deficiency mimicking Leigh syndrome associated with methylmalonic aciduriaGiulia Ferrera, Sara Boenzi, Eleonora Lamantea, et al.
Molecular Genetics and Metabolism|June 15, 2013
Optimizing the dose of hydroxocobalamin in cobalamin C (cblC) defectCarlo Dionisi-Vici, Diego Martinelli, Ferdinando Ceravolo, et al.
Frontiers in Pediatrics|January 21, 2025
Case Report: Two years of compassionate use with Olipudase-alfa in a child with neurovisceral acid sphingomyelinase deficiencyFederica Deodato, Sara Boenzi, Benedetta Greco, et al.
Molecular Genetics and Metabolism|November 23, 2021
Comprehensive-targeted lipidomic analysis in Niemann-Pick C diseaseSara Boenzi, Giulio Catesini, Elisa Sacchetti, et al.
Journal of Lipid Research|January 7, 2016
Evaluation of plasma cholestane-3β,5α,6β-triol and 7-ketocholesterol in inherited disorders related to cholesterol metabolismSara Boenzi, Federica Deodato, Roberta Taurisano, et al.
Ophthalmology|August 5, 2009
Retinal degenerationChiara Morini, Paolo Capozzi, Sara Boenzi, et al.
Journal of Lipid Research|December 22, 2025
New Multiplex LC-MS/MS Method for lipid biomarker Analysis of Inherited Neurodegenerative Metabolic DiseasesAnna Sidorina, Giulio Catesini, Federica Deodato, et al.
Clinica Chimica Acta; International Journal of Clinical Chemistry|May 19, 2016
A new multiplex method for the diagnosis of peroxisomal disorders allowing simultaneous determination of plasma very-long-chain fatty acids, phytanic, pristanic, docosahexaenoic and bile acids by high-performance liquid chromatography-atmospheric pressure chemical ionization-tandem mass spectrometryMichela Semeraro, Cristiano Rizzo, Sara Boenzi, et al.
Pageof 5