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Brain & Development|January 16, 2010
The effect of N-octyl-β-valienamine on β-glucosidase activity in tissues of normal miceZhuo Luan, Haruaki Ninomiya, Kousaku Ohno, et al.Brain & Development|April 18, 2006
Fibroblast screening for chaperone therapy in beta-galactosidosisHiroyuki Iwasaki, Hiroshi Watanabe, Masami Iida, et al.Blood Cells, Molecules & Diseases|October 28, 2009
The pharmacological chaperone effect of N-octyl-beta-valienamine on human mutant acid beta-glucosidasesZhuo Luan, Linjing Li, Haruaki Ninomiya, et al.Molecular Genetics and Metabolism|September 10, 2010
Chemical chaperone therapy: luciferase assay for screening of β-galactosidase mutationsLinjing Li, Katsumi Higaki, Haruaki Ninomiya, et al.Organic & Biomolecular Chemistry|March 10, 2004
Convenient synthesis of (+)-valiolamine and (-)-1-epi-valiolamine from (-)-vibo-quercitolSeiichiro Ogawa, Yo Ohishi, Miwako Asada, et al.Bioorganic & Medicinal Chemistry|November 24, 2004
Synthesis and glycosidase inhibitory activity of some N-substituted 5a-carba-beta-fuco- and beta-galactopyranosylamines, and selected derivativesSeiichiro Ogawa, Shigeo Fujieda, Yuko Sakata, et al.Biochimica Et Biophysica Acta|March 17, 2007
Enzyme enhancement activity of N-octyl-beta-valienamine on beta-glucosidase mutants associated with Gaucher diseaseKe Lei, Haruaki Ninomiya, Michitaka Suzuki, et al.Molecular Genetics and Metabolism|March 23, 2012
Therapeutic chaperone effect of N-octyl 4-epi-β-valienamine on murine G(M1)-gangliosidosisYoshiyuki Suzuki, Satoshi Ichinomiya, Mieko Kurosawa, et al.Biochimica Et Biophysica Acta|July 28, 2004
N-octyl-beta-valienamine up-regulates activity of F213I mutant beta-glucosidase in cultured cells: a potential chemical chaperone therapy for Gaucher diseaseHou Lin, Yuko Sugimoto, Yuki Ohsaki, et al.Annals of Neurology|November 13, 2007
Chemical chaperone therapy: clinical effect in murine G(M1)-gangliosidosisYoshiyuki Suzuki, Satoshi Ichinomiya, Mieko Kurosawa, et al.Pageof 4