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Human Genetics|July 7, 2021
Human deafness-associated variants alter the dynamics of key molecules in hair cell stereocilia F-actin coresTakushi Miyoshi, Inna A Belyantseva, Shin-Ichiro Kitajiri, et al.
EMBO Molecular Medicine|October 7, 2016
Constitutive activation of DIA1 (DIAPH1) via C-terminal truncation causes human sensorineural hearing lossTakehiko Ueyama, Yuzuru Ninoyu, Shin-Ya Nishio, et al.
Scientific Reports|April 23, 2020
Cochlear supporting cells function as macrophage-like cells and protect audiosensory receptor hair cells from pathogensYushi Hayashi, Hidenori Suzuki, Wataru Nakajima, et al.
Scientific Reports|April 29, 2020
Novel ACTG1 mutations in patients identified by massively parallel DNA sequencing cause progressive hearing lossHiroki Miyajima, Hideaki Moteki, Timothy Day, et al.
Genes|September 19, 2019
Mid-Frequency Hearing Loss Is Characteristic Clinical Feature of <i>OTOA</i>-Associated Hearing LossKenjiro Sugiyama, Hideaki Moteki, Shin-Ichiro Kitajiri, et al.
Plos One|November 29, 2021
Virus-infection in cochlear supporting cells induces audiosensory receptor hair cell death by TRAIL-induced necroptosisYushi Hayashi, Hidenori Suzuki, Wataru Nakajima, et al.
Human Mutation|January 18, 2007
Mutations of the RDX gene cause nonsyndromic hearing loss at the DFNB24 locusShahid Y Khan, Zubair M Ahmed, Muhammad I Shabbir, et al.
American Journal of Human Genetics|December 23, 2006
Tricellulin is a tight-junction protein necessary for hearingSaima Riazuddin, Zubair M Ahmed, Alan S Fanning, et al.
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