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Simon C Johnson

Showing results (21-30 of 42) with videos related to

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Orphanet Journal of Rare Diseases|February 10, 2025
Evaluating the efficacy of vatiquinone in preclinical models of Leigh syndrome and GPX4 deficiencyErnst-Bernhard Kayser, Michael Mulholland, Elizaveta A Olkhova, et al.
Orphanet Journal of Rare Diseases|September 4, 2023
Leigh syndrome global patient registry: uniting patients and researchers worldwideSophia Zilber, Kasey Woleben, Simon C Johnson, et al.
Molecular Genetics and Metabolism|April 26, 2020
Regional metabolic signatures in the Ndufs4(KO) mouse brain implicate defective glutamate/α-ketoglutarate metabolism in mitochondrial diseaseSimon C Johnson, Ernst-Bernhard Kayser, Rebecca Bornstein, et al.
Brain Pathology (Zurich, Switzerland)|August 8, 2023
Peripheral macrophages drive CNS disease in the Ndufs4(-/-) model of Leigh syndromeAllison R Hanaford, Asheema Khanna, Vivian Truong, et al.
Plos One|March 22, 2019
Relevance of experimental paradigms of anesthesia induced neurotoxicity in the mouseSimon C Johnson, Amanda Pan, Grace X Sun, et al.
Plos One|June 10, 2025
Disruption of adaptive immunity does not attenuate disease in the Ndufs4(-/-) model of Leigh syndromeAllison R Hanaford, Asheema Khanna, Vivian Truong, et al.
JCI Insight|January 20, 2022
Leukocytes mediate disease pathogenesis in the Ndufs4(KO) mouse model of Leigh syndromeJulia C Stokes, Rebecca L Bornstein, Katerina James, et al.
Paediatric Anaesthesia|February 15, 2024
Impact of dietary ketosis on volatile anesthesia toxicity in a model of Leigh syndromeKira A Spencer, Miranda N Howe, Michael T Mulholland, et al.
Orphanet Journal of Rare Diseases|October 24, 2021
Development of therapies for rare genetic disorders of GPX4: roadmap and opportunitiesDorian M Cheff, Alysson R Muotri, Brent R Stockwell, et al.
Elife|July 13, 2021
Mechanisms underlying neonate-specific metabolic effects of volatile anestheticsJulia Stokes, Arielle Freed, Rebecca Bornstein, et al.
Pageof 5

Showing results (21-30 of 42) with videos related to

Sort By:
Pageof 5
Orphanet Journal of Rare Diseases|February 10, 2025
Evaluating the efficacy of vatiquinone in preclinical models of Leigh syndrome and GPX4 deficiencyErnst-Bernhard Kayser, Michael Mulholland, Elizaveta A Olkhova, et al.
Orphanet Journal of Rare Diseases|September 4, 2023
Leigh syndrome global patient registry: uniting patients and researchers worldwideSophia Zilber, Kasey Woleben, Simon C Johnson, et al.
Molecular Genetics and Metabolism|April 26, 2020
Regional metabolic signatures in the Ndufs4(KO) mouse brain implicate defective glutamate/α-ketoglutarate metabolism in mitochondrial diseaseSimon C Johnson, Ernst-Bernhard Kayser, Rebecca Bornstein, et al.
Brain Pathology (Zurich, Switzerland)|August 8, 2023
Peripheral macrophages drive CNS disease in the Ndufs4(-/-) model of Leigh syndromeAllison R Hanaford, Asheema Khanna, Vivian Truong, et al.
Plos One|March 22, 2019
Relevance of experimental paradigms of anesthesia induced neurotoxicity in the mouseSimon C Johnson, Amanda Pan, Grace X Sun, et al.
Plos One|June 10, 2025
Disruption of adaptive immunity does not attenuate disease in the Ndufs4(-/-) model of Leigh syndromeAllison R Hanaford, Asheema Khanna, Vivian Truong, et al.
JCI Insight|January 20, 2022
Leukocytes mediate disease pathogenesis in the Ndufs4(KO) mouse model of Leigh syndromeJulia C Stokes, Rebecca L Bornstein, Katerina James, et al.
Paediatric Anaesthesia|February 15, 2024
Impact of dietary ketosis on volatile anesthesia toxicity in a model of Leigh syndromeKira A Spencer, Miranda N Howe, Michael T Mulholland, et al.
Orphanet Journal of Rare Diseases|October 24, 2021
Development of therapies for rare genetic disorders of GPX4: roadmap and opportunitiesDorian M Cheff, Alysson R Muotri, Brent R Stockwell, et al.
Elife|July 13, 2021
Mechanisms underlying neonate-specific metabolic effects of volatile anestheticsJulia Stokes, Arielle Freed, Rebecca Bornstein, et al.
Pageof 5