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Showing results (81-90 of 169) with videos related to

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European Journal of Pediatrics|February 1, 1986
Impaired plasmalogen metabolism in infantile Refsum's diseaseB T Poll-Thé, H Ogier, J M Saudubray, et al.
Journal of Inherited Metabolic Disease|January 1, 1991
A new type of chondrodysplasia punctata associated with peroxisomal dysfunctionB T Poll-The, P Maroteaux, C Narcy, et al.
Clinical Genetics|September 1, 2017
Development and validation of a severity scoring system for Zellweger spectrum disordersF C C Klouwer, A Meester-Delver, F M Vaz, et al.
Scandinavian Journal of Clinical and Laboratory Investigation. Supplementum|January 1, 1993
Peroxisomal beta-oxidation of polyunsaturated long chain fatty acids in human fibroblasts. The polyunsaturated and the saturated long chain fatty acids are retroconverted by the same acyl-CoA oxidaseE Christensen, B Woldseth, T A Hagve, et al.
Human Mutation|June 20, 1998
Spectrum of mutations in the fumarylacetoacetate hydrolase gene of tyrosinemia type 1 patients in northwestern Europe and Mediterranean countriesA J Bergman, I E van den Berg, W Brink, et al.
Journal of Inherited Metabolic Disease|May 29, 2007
Renal Fanconi syndrome with ultrastructural defects in lysinuric protein intoleranceM A Benninga, M Lilien, T J de Koning, et al.
European Journal of Human Genetics : EJHG|July 26, 2000
Mutation detection in the aspartoacylase gene in 17 patients with Canavan disease: four new mutations in the non-Jewish populationE A Sistermans, R F de Coo, H M van Beerendonk, et al.
Journal of Inherited Metabolic Disease|February 11, 2005
Increasing fat in the diet does not improve muscle performance in patients with mitochondrial myopathy due to complex I deficiencyK de Meer, M J Roef, J B C de Klerk, et al.
European Journal of Human Genetics : EJHG|April 21, 2001
A Rett syndrome patient with a ring X chromosome: further evidence for skewing of X inactivation and heterogeneity in the aetiology of the diseaseC Rosenberg, C H Wouters, K Szuhai, et al.
Journal of Lipid Research|November 4, 2000
Pristanic acid and phytanic acid: naturally occurring ligands for the nuclear receptor peroxisome proliferator-activated receptor alphaA W Zomer, B van Der Burg, G A Jansen, et al.
Pageof 17

Showing results (81-90 of 169) with videos related to

Sort By:
Pageof 17
European Journal of Pediatrics|February 1, 1986
Impaired plasmalogen metabolism in infantile Refsum's diseaseB T Poll-Thé, H Ogier, J M Saudubray, et al.
Journal of Inherited Metabolic Disease|January 1, 1991
A new type of chondrodysplasia punctata associated with peroxisomal dysfunctionB T Poll-The, P Maroteaux, C Narcy, et al.
Clinical Genetics|September 1, 2017
Development and validation of a severity scoring system for Zellweger spectrum disordersF C C Klouwer, A Meester-Delver, F M Vaz, et al.
Scandinavian Journal of Clinical and Laboratory Investigation. Supplementum|January 1, 1993
Peroxisomal beta-oxidation of polyunsaturated long chain fatty acids in human fibroblasts. The polyunsaturated and the saturated long chain fatty acids are retroconverted by the same acyl-CoA oxidaseE Christensen, B Woldseth, T A Hagve, et al.
Human Mutation|June 20, 1998
Spectrum of mutations in the fumarylacetoacetate hydrolase gene of tyrosinemia type 1 patients in northwestern Europe and Mediterranean countriesA J Bergman, I E van den Berg, W Brink, et al.
Journal of Inherited Metabolic Disease|May 29, 2007
Renal Fanconi syndrome with ultrastructural defects in lysinuric protein intoleranceM A Benninga, M Lilien, T J de Koning, et al.
European Journal of Human Genetics : EJHG|July 26, 2000
Mutation detection in the aspartoacylase gene in 17 patients with Canavan disease: four new mutations in the non-Jewish populationE A Sistermans, R F de Coo, H M van Beerendonk, et al.
Journal of Inherited Metabolic Disease|February 11, 2005
Increasing fat in the diet does not improve muscle performance in patients with mitochondrial myopathy due to complex I deficiencyK de Meer, M J Roef, J B C de Klerk, et al.
European Journal of Human Genetics : EJHG|April 21, 2001
A Rett syndrome patient with a ring X chromosome: further evidence for skewing of X inactivation and heterogeneity in the aetiology of the diseaseC Rosenberg, C H Wouters, K Szuhai, et al.
Journal of Lipid Research|November 4, 2000
Pristanic acid and phytanic acid: naturally occurring ligands for the nuclear receptor peroxisome proliferator-activated receptor alphaA W Zomer, B van Der Burg, G A Jansen, et al.
Pageof 17