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U Wendel

Showing results (171-180 of 186) with videos related to

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Monatsschrift Kinderheilkunde : Organ Der Deutschen Gesellschaft Fur Kinderheilkunde|November 1, 1991
[Macrocephaly as the initial manifestation of glutaryl-CoA-dehydrogenase deficiency (glutaric aciduria type I)]F K Trefz, G F Hoffmann, E Mayatepek, et al.
Journal of Inherited Metabolic Disease|January 1, 1994
Molecular genetic characterization and urinary excretion pattern of metabolites in two families with MCAD deficiency due to compound heterozygosity with a 13 base pair insertion in one alleleN Gregersen, V Winter, S Lyonnet, et al.
Journal of Inherited Metabolic Disease|June 10, 2006
Carnitine supplementation induces long-chain acylcarnitine production--studies in the VLCAD-deficient mouseM Liebig, M Gyenes, G Brauers, et al.
Journal of Inherited Metabolic Disease|January 29, 2013
Structural white matter changes in adolescents and young adults with maple syrup urine diseaseD Klee, E Thimm, H J Wittsack, et al.
Biochimica Et Biophysica Acta|October 19, 1999
beta-Trace protein in human cerebrospinal fluid: a diagnostic marker for N-glycosylation defects in brainS Grünewald, K Huyben, J G de Jong, et al.
European Journal of Human Genetics : EJHG|September 14, 1999
The putative glucose 6-phosphate translocase gene is mutated in essentially all cases of glycogen storage disease type I non-aM Veiga-da-Cunha, I Gerin, Y T Chen, et al.
Neuropediatrics|September 26, 2001
Infantile presentation of the mtDNA A3243G tRNA(Leu (UUR)) mutationE J Okhuijsen-Kroes, J M Trijbels, R C Sengers, et al.
Journal of Inherited Metabolic Disease|January 1, 1995
Liver transplantation in two cases of propionic acidaemiaJ S Schlenzig, F Poggi-Travert, J Laurent, et al.
Journal of the Neurological Sciences|July 1, 1997
Clinical heterogeneity in respiratory chain complex III deficiency in childhoodJ Mourmans, U Wendel, H A Bentlage, et al.
Pediatric Research|May 1, 1996
Deficiency of the voltage-dependent anion channel: a novel cause of mitochondriopathyM Huizing, W Ruitenbeek, F P Thinnes, et al.
Pageof 19

Showing results (171-180 of 186) with videos related to

Sort By:
Pageof 19
Monatsschrift Kinderheilkunde : Organ Der Deutschen Gesellschaft Fur Kinderheilkunde|November 1, 1991
[Macrocephaly as the initial manifestation of glutaryl-CoA-dehydrogenase deficiency (glutaric aciduria type I)]F K Trefz, G F Hoffmann, E Mayatepek, et al.
Journal of Inherited Metabolic Disease|January 1, 1994
Molecular genetic characterization and urinary excretion pattern of metabolites in two families with MCAD deficiency due to compound heterozygosity with a 13 base pair insertion in one alleleN Gregersen, V Winter, S Lyonnet, et al.
Journal of Inherited Metabolic Disease|June 10, 2006
Carnitine supplementation induces long-chain acylcarnitine production--studies in the VLCAD-deficient mouseM Liebig, M Gyenes, G Brauers, et al.
Journal of Inherited Metabolic Disease|January 29, 2013
Structural white matter changes in adolescents and young adults with maple syrup urine diseaseD Klee, E Thimm, H J Wittsack, et al.
Biochimica Et Biophysica Acta|October 19, 1999
beta-Trace protein in human cerebrospinal fluid: a diagnostic marker for N-glycosylation defects in brainS Grünewald, K Huyben, J G de Jong, et al.
European Journal of Human Genetics : EJHG|September 14, 1999
The putative glucose 6-phosphate translocase gene is mutated in essentially all cases of glycogen storage disease type I non-aM Veiga-da-Cunha, I Gerin, Y T Chen, et al.
Neuropediatrics|September 26, 2001
Infantile presentation of the mtDNA A3243G tRNA(Leu (UUR)) mutationE J Okhuijsen-Kroes, J M Trijbels, R C Sengers, et al.
Journal of Inherited Metabolic Disease|January 1, 1995
Liver transplantation in two cases of propionic acidaemiaJ S Schlenzig, F Poggi-Travert, J Laurent, et al.
Journal of the Neurological Sciences|July 1, 1997
Clinical heterogeneity in respiratory chain complex III deficiency in childhoodJ Mourmans, U Wendel, H A Bentlage, et al.
Pediatric Research|May 1, 1996
Deficiency of the voltage-dependent anion channel: a novel cause of mitochondriopathyM Huizing, W Ruitenbeek, F P Thinnes, et al.
Pageof 19