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Vincent Procaccio

Showing results (91-100 of 197) with videos related to

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European Journal of Human Genetics : EJHG|September 20, 2012
Refractory epilepsy and mitochondrial dysfunction due to GM3 synthase deficiencyKonstantina Fragaki, Samira Ait-El-Mkadem, Annabelle Chaussenot, et al.
Placenta|June 27, 2018
Study of mitochondrial function in placental insufficiencyTiphaine Lefebvre, Ombeline Roche, Valérie Seegers, et al.
BMC Research Notes|December 24, 2011
Idebenone increases mitochondrial complex I activity in fibroblasts from LHON patients while producing contradictory effects on respirationClaire Angebault, Naïg Gueguen, Valérie Desquiret-Dumas, et al.
Orphanet Journal of Rare Diseases|February 19, 2018
Cyclosporine A does not prevent second-eye involvement in Leber's hereditary optic neuropathyStéphanie Leruez, Christophe Verny, Dominique Bonneau, et al.
The International Journal of Biochemistry & Cell Biology|April 25, 2009
OPA1-associated disorders: phenotypes and pathophysiologyPatrizia Amati-Bonneau, Dan Milea, Dominique Bonneau, et al.
Neuroscience Letters|July 1, 2009
Mitochondrial dysfunction in CA1 hippocampal neurons of the UBE3A deficient mouse model for Angelman syndromeHailing Su, Weiwei Fan, Pinar E Coskun, et al.
Biochimica Et Biophysica Acta. Molecular Basis of Disease|November 6, 2016
The addition of ketone bodies alleviates mitochondrial dysfunction by restoring complex I assembly in a MELAS cellular modelSamuel Frey, Guillaume Geffroy, Valerie Desquiret-Dumas, et al.
The Journal of Biological Chemistry|November 2, 2013
Resveratrol induces a mitochondrial complex I-dependent increase in NADH oxidation responsible for sirtuin activation in liver cellsValérie Desquiret-Dumas, Naïg Gueguen, Géraldine Leman, et al.
Annals of Neurology|September 27, 2002
Aggregation of actin and cofilin in identical twins with juvenile-onset dystoniaMarla Gearing, Jorge L Juncos, Vincent Procaccio, et al.
Neurogenetics|December 18, 2008
Mitochondrial complex I deficiency in GDAP1-related autosomal dominant Charcot-Marie-Tooth disease (CMT2K)Julien Cassereau, Arnaud Chevrollier, Naïg Gueguen, et al.
Pageof 20

Showing results (91-100 of 197) with videos related to

Sort By:
Pageof 20
European Journal of Human Genetics : EJHG|September 20, 2012
Refractory epilepsy and mitochondrial dysfunction due to GM3 synthase deficiencyKonstantina Fragaki, Samira Ait-El-Mkadem, Annabelle Chaussenot, et al.
Placenta|June 27, 2018
Study of mitochondrial function in placental insufficiencyTiphaine Lefebvre, Ombeline Roche, Valérie Seegers, et al.
BMC Research Notes|December 24, 2011
Idebenone increases mitochondrial complex I activity in fibroblasts from LHON patients while producing contradictory effects on respirationClaire Angebault, Naïg Gueguen, Valérie Desquiret-Dumas, et al.
Orphanet Journal of Rare Diseases|February 19, 2018
Cyclosporine A does not prevent second-eye involvement in Leber's hereditary optic neuropathyStéphanie Leruez, Christophe Verny, Dominique Bonneau, et al.
The International Journal of Biochemistry & Cell Biology|April 25, 2009
OPA1-associated disorders: phenotypes and pathophysiologyPatrizia Amati-Bonneau, Dan Milea, Dominique Bonneau, et al.
Neuroscience Letters|July 1, 2009
Mitochondrial dysfunction in CA1 hippocampal neurons of the UBE3A deficient mouse model for Angelman syndromeHailing Su, Weiwei Fan, Pinar E Coskun, et al.
Biochimica Et Biophysica Acta. Molecular Basis of Disease|November 6, 2016
The addition of ketone bodies alleviates mitochondrial dysfunction by restoring complex I assembly in a MELAS cellular modelSamuel Frey, Guillaume Geffroy, Valerie Desquiret-Dumas, et al.
The Journal of Biological Chemistry|November 2, 2013
Resveratrol induces a mitochondrial complex I-dependent increase in NADH oxidation responsible for sirtuin activation in liver cellsValérie Desquiret-Dumas, Naïg Gueguen, Géraldine Leman, et al.
Annals of Neurology|September 27, 2002
Aggregation of actin and cofilin in identical twins with juvenile-onset dystoniaMarla Gearing, Jorge L Juncos, Vincent Procaccio, et al.
Neurogenetics|December 18, 2008
Mitochondrial complex I deficiency in GDAP1-related autosomal dominant Charcot-Marie-Tooth disease (CMT2K)Julien Cassereau, Arnaud Chevrollier, Naïg Gueguen, et al.
Pageof 20