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Wangzhen Shen

Showing results (21-30 of 52) with videos related to

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Brain Communications|August 1, 2022
4-Phenylbutyrate restored γ-aminobutyric acid uptake and reduced seizures in <i>SLC6A1</i> patient variant-bearing cell and mouse modelsGerald Nwosu, Felicia Mermer, Carson Flamm, et al.
Circulation Research|September 21, 2002
Phosphorylation and putative ER retention signals are required for protein kinase A-mediated potentiation of cardiac sodium currentJingsong Zhou, Hyeon-Gyu Shin, Jianxun Yi, et al.
Annals of Clinical and Translational Neurology|May 20, 2026
Unraveling 4-Phenylbutyrate's Therapeutic Role in SLC6A1 Disorders: Pharmacochaperoning Over HDAC InhibitionMelissa B DeLeeuw, Karishma Randhave, Ekta Anand, et al.
Scientific Reports|October 21, 2016
Differential protein structural disturbances and suppression of assembly partners produced by nonsense GABRG2 epilepsy mutations: implications for disease phenotypic heterogeneityJuexin Wang, Dingding Shen, Geqing Xia, et al.
Brain Communications|May 30, 2020
GABA<sub>A</sub> receptor β3 subunit mutation D120N causes Lennox-Gastaut syndrome in knock-in miceShimian Qu, Mackenzie Catron, Chengwen Zhou, et al.
Experimental Neurology|May 7, 2021
Genetic mosaicism, intrafamilial phenotypic heterogeneity, and molecular defects of a novel missense SLC6A1 mutation associated with epilepsy and ADHDSarah Poliquin, Inna Hughes, Wangzhen Shen, et al.
Epilepsia|June 7, 2017
Overexpressing wild-type γ2 subunits rescued the seizure phenotype in Gabrg2<sup>+/Q390X</sup> Dravet syndrome miceXuan Huang, Chengwen Zhou, Mengnan Tian, et al.
Neurobiology of Disease|October 17, 2012
Impaired surface αβγ GABA(A) receptor expression in familial epilepsy due to a GABRG2 frameshift mutationMengnan Tian, Davide Mei, Elena Freri, et al.
Epilepsia|May 16, 2019
Molecular basis for and chemogenetic modulation of comorbidities in GABRG2-deficient epilepsiesChun-Qing Zhang, Bryan McMahon, Huancheng Dong, et al.
Eneuro|February 16, 2017
Altered Channel Conductance States and Gating of GABA<sub>A</sub> Receptors by a Pore Mutation Linked to Dravet SyndromeCiria C Hernandez, Weijing Kong, Ningning Hu, et al.
Pageof 6

Showing results (21-30 of 52) with videos related to

Sort By:
Pageof 6
Brain Communications|August 1, 2022
4-Phenylbutyrate restored γ-aminobutyric acid uptake and reduced seizures in <i>SLC6A1</i> patient variant-bearing cell and mouse modelsGerald Nwosu, Felicia Mermer, Carson Flamm, et al.
Circulation Research|September 21, 2002
Phosphorylation and putative ER retention signals are required for protein kinase A-mediated potentiation of cardiac sodium currentJingsong Zhou, Hyeon-Gyu Shin, Jianxun Yi, et al.
Annals of Clinical and Translational Neurology|May 20, 2026
Unraveling 4-Phenylbutyrate's Therapeutic Role in SLC6A1 Disorders: Pharmacochaperoning Over HDAC InhibitionMelissa B DeLeeuw, Karishma Randhave, Ekta Anand, et al.
Scientific Reports|October 21, 2016
Differential protein structural disturbances and suppression of assembly partners produced by nonsense GABRG2 epilepsy mutations: implications for disease phenotypic heterogeneityJuexin Wang, Dingding Shen, Geqing Xia, et al.
Brain Communications|May 30, 2020
GABA<sub>A</sub> receptor β3 subunit mutation D120N causes Lennox-Gastaut syndrome in knock-in miceShimian Qu, Mackenzie Catron, Chengwen Zhou, et al.
Experimental Neurology|May 7, 2021
Genetic mosaicism, intrafamilial phenotypic heterogeneity, and molecular defects of a novel missense SLC6A1 mutation associated with epilepsy and ADHDSarah Poliquin, Inna Hughes, Wangzhen Shen, et al.
Epilepsia|June 7, 2017
Overexpressing wild-type γ2 subunits rescued the seizure phenotype in Gabrg2<sup>+/Q390X</sup> Dravet syndrome miceXuan Huang, Chengwen Zhou, Mengnan Tian, et al.
Neurobiology of Disease|October 17, 2012
Impaired surface αβγ GABA(A) receptor expression in familial epilepsy due to a GABRG2 frameshift mutationMengnan Tian, Davide Mei, Elena Freri, et al.
Epilepsia|May 16, 2019
Molecular basis for and chemogenetic modulation of comorbidities in GABRG2-deficient epilepsiesChun-Qing Zhang, Bryan McMahon, Huancheng Dong, et al.
Eneuro|February 16, 2017
Altered Channel Conductance States and Gating of GABA<sub>A</sub> Receptors by a Pore Mutation Linked to Dravet SyndromeCiria C Hernandez, Weijing Kong, Ningning Hu, et al.
Pageof 6