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David Smith

6PUBLICATIONS

13CO-AUTHORS

AutoimmunityCellular nervous systemNutrigenomics and personalised nutritionNeurology and neuromuscular diseasesProsthetics and orthotics

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Publications (6)

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|Jan 10, 2025

Dysregulation of the NLRP3 Inflammasome and Promotion of Disease by IL-1β in a Murine Model of Sandhoff Disease.

Nick Platt, Dawn Shepherd, David A Smith

|Jun 28, 2023

A Novel Small <i>NPC1</i> Promoter Enhances AAV-Mediated Gene Therapy in Mouse Models of Niemann-Pick Type C1 Disease.

Michael Paul Hughes, Hemanth Ramesh Nelvagal, Oliver Coombe-Tennant

|Apr 18, 2023

Defective iron homeostasis and hematological abnormalities in Niemann-Pick disease type C1.

Oscar C W Chen, Stephan Siebel, Alexandria Colaco

|Jun 13, 2022

Anti-TNF therapy for inflammatory bowel disease in patients with neurodegenerative Niemann-Pick disease Type C.

Isabelle Williams, Sumeet Pandey, Wolfram Haller

|Apr 12, 2020

Beneficial Effects of Acetyl-DL-Leucine (ADLL) in a Mouse Model of Sandhoff Disease.

Ecem Kaya, David A Smith, Claire Smith

|Oct 25, 2017

Differential response of the liver to bile acid treatment in a mouse model of Niemann-Pick disease type C.

Elena-Raluca Nicoli, Mylene Huebecker, David Smith

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Frequent Collaborators

6 joint publications

Frances Mary Platt

2 joint publications

Elena-Raluca Nicoli

1 joint publications

Hemanth Ramesh Nelvagal

1 joint publications

Giulia Massaro

1 joint publications

Ahad Abdul Rahim

1 joint publications

Ecem Kaya

1 joint publications

Barry Boland

1 joint publications

Dawn Shepherd

1 joint publications

Andrew E Armitage

1 joint publications

Kerri-Lee Wallom

Frequent Collaborators

6 joint publications

Frances Mary Platt

2 joint publications

Elena-Raluca Nicoli

1 joint publications

Hemanth Ramesh Nelvagal

1 joint publications

Giulia Massaro

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