Jonathan D Cooper

14PUBLICATIONS
43CO-AUTHORS
Central nervous systemNeurology and neuromuscular diseasesKnowledge representation and reasoningTransplantation immunologyComputational neuroscience (incl. mathematical neuroscience and theoretical neuroscience)
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Publications (14)

|May 18, 2026
<i>In vivo</i> BMAL1 occupancy mapping using MACS-Calling Cards reveals disease-associated retargeting in <i>Cln3</i> <sup><i>Δex7/8</i></sup> astrocytes.

|Apr 14, 2026
Systemic AAV9 Gene Therapy Mitigates Neuromuscular Junction Degeneration and Muscle Atrophy in a Mouse Model of CLN1 Disease.

Ewa A Ziółkowska, Albina Jablonka-Shariff, Letitia L Williams

|Sep 04, 2025
Neuronal ceroid lipofuscinosis: underlying mechanisms and emerging therapeutic targets.

Ewa A Ziółkowska, Keigo Takahashi, Patricia I Dickson

|Aug 16, 2025
Enteric nervous system disease in neuronopathic lysosomal storage disorders.

Ewa A Ziółkowska, Robert O Heuckeroth, Jonathan D Cooper

|Feb 20, 2025
Enteric nervous system degeneration in human and murine CLN3 disease, is ameliorated by gene therapy in mice.

Ewa A Ziółkowska, Letitia L Williams, Matthew J Jansen

|Jan 15, 2025
Gene therapy ameliorates bowel dysmotility and enteric neuron degeneration and extends survival in lysosomal storage disorder mouse models.

Ewa A Ziółkowska, Matthew J Jansen, Letitia L Williams

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Frequent Collaborators

4 joint publications

Mark S Sands

4 joint publications

Ewa A Ziółkowska

3 joint publications

Letitia L Williams

3 joint publications

Keigo Takahashi