Jonathan D Cooper

14PUBLICATIONS

43CO-AUTHORS

Central nervous systemNeurology and neuromuscular diseasesKnowledge representation and reasoningTransplantation immunologyComputational neuroscience (incl. mathematical neuroscience and theoretical neuroscience)

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Publications (14)

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|May 18, 2026

In vivo BMAL1 occupancy mapping using MACS-Calling Cards reveals disease-associated retargeting in Cln3 Δex7/8 astrocytes.

|Apr 14, 2026

Systemic AAV9 Gene Therapy Mitigates Neuromuscular Junction Degeneration and Muscle Atrophy in a Mouse Model of CLN1 Disease.

Ewa A Ziółkowska, Albina Jablonka-Shariff, Letitia L Williams

|Sep 04, 2025

Neuronal ceroid lipofuscinosis: underlying mechanisms and emerging therapeutic targets.

Ewa A Ziółkowska, Keigo Takahashi, Patricia I Dickson

|Aug 16, 2025

Enteric nervous system disease in neuronopathic lysosomal storage disorders.

Ewa A Ziółkowska, Robert O Heuckeroth, Jonathan D Cooper

|Feb 20, 2025

Enteric nervous system degeneration in human and murine CLN3 disease, is ameliorated by gene therapy in mice.

Ewa A Ziółkowska, Letitia L Williams, Matthew J Jansen

|Jan 15, 2025

Gene therapy ameliorates bowel dysmotility and enteric neuron degeneration and extends survival in lysosomal storage disorder mouse models.

Ewa A Ziółkowska, Matthew J Jansen, Letitia L Williams

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Frequent Collaborators

Mark S Sands

Ewa A Ziółkowska

Letitia L Williams

Keigo Takahashi

Hemanth R Nelvagal

Ineka T Whiteman

Rebecca P Bradley

Matthew J Jansen

Patricia I Dickson

Jaiprakash Sharma

Frequent Collaborators

Mark S Sands

Ewa A Ziółkowska

Letitia L Williams

Keigo Takahashi