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Congenital vulvar lymphangioma circumscriptum

Yilmaz Dikmen1, Mustafa Coşan Terek, Levent Akman

  • 1Department of Obstetrics and Gynecology, Ege University Faculty of Medicine, Bornova, Izmir 35260, Turkey.

International Journal of Clinical Oncology
|October 24, 2008
PubMed

Insights

Lymphangioma circumscriptum, a rare lymphatic malformation, can present as a vulvar mass. This case highlights the importance of considering this condition in elderly patients with vulvar lesions and leg swelling.

Area of Science:

  • Dermatology
  • Vascular Malformations
  • Gynecologic Oncology

Background:

  • Lymphangioma circumscriptum (LC) is a rare congenital lymphatic malformation.
  • It typically presents as grouped vesicles on the skin surface.
  • LC rarely affects the vulvar region.

Observation:

  • A 72-year-old patient presented with a vulvar mass.
  • The patient also exhibited ipsilateral leg edema.
  • The vulvar mass was diagnosed as Lymphangioma circumscriptum.

Findings:

  • This case represents a rare occurrence of vulvar Lymphangioma circumscriptum.
  • The presentation included a vulvar mass and associated leg swelling.
  • Diagnostic imaging and biopsy confirmed the lymphatic malformation.

Implications:

  • This case expands the known clinical spectrum of vulvar lymphatic malformations.
  • It underscores the need for a high index of suspicion for LC in elderly patients with vulvar masses.
  • Early diagnosis and management are crucial for patient outcomes.

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