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Isolated chylopericardium secondary to intrathymic lymphangiomatous malformation
R Dogan1, M Demircin, A Sarigül
1Department of Thoracic and Cardiovascular Surgery, Hacettepe University, School of Medicine, Ankara, Turkey.
Insights
Chylopericardium, a rare condition, was successfully treated in a young patient with a thymic lymphangiomatous malformation. Surgical excision of the malformation and pericardiectomy resolved the recurrent pericardial effusion.
Area of Science:
- Cardiology
- Thoracic Surgery
- Pediatric Pathology
Background:
- Chylopericardium is a rare condition characterized by the accumulation of chyle in the pericardial sac.
- Lymphangiomatous malformations, particularly in the thymus, are uncommon causes of chylopericardium.
Observation:
- A case of chylopericardium in a 2-year-old patient is presented.
- Diagnosis was confirmed via pericardiocentesis and fluid analysis.
- Recurrent pericardial effusion necessitated surgical intervention.
Findings:
- The patient underwent pericardiectomy and excision of an intrathymic ectatic lymphangiomatous malformation.
- Pathologic examination revealed diffuse hyperplasia and a tumor within the thymus.
- The patient recovered fully without chyle reaccumulation.
Implications:
- This case highlights the importance of considering intrathymic lymphangiomatous malformations in pediatric chylopericardium.
- Surgical management, including thymectomy and pericardiectomy, can be curative.
- Early diagnosis and intervention are crucial for favorable outcomes in rare pediatric thoracic conditions.
Abstract:
A case of chylopericardium associated with lymphangiomatous malformation of the thymus is presented. The specific diagnosis of chylopericardium was made by pericardiocentesis and analysis of the fluid. Despite the pericardiocentesis and pericardial tube drainage, pericardial effusion recurred and the patient underwent pericardiectomy. At operation the thymus, which contained a tumor and showed diffuse hyperplasia, was excised and pericardiectomy was performed. The 2-year-old patient recovered uneventfully without reaccumulation of the chyle. The pathologic diagnosis of the mass was intrathymic ectatic lymphangiomatous malformation.
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