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Updated: Jul 24, 2026

Investigating the Spreading and Toxicity of Prion-like Proteins Using the Metazoan Model Organism C. elegans
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Biología molecular de las enfermedades priónicas

S B Prusiner1

  • 1Department of Neurology, University of California, San Francisco 94143.

Science (New York, N.Y.)
|June 14, 1991
PubMed
Resumen

Las enfermedades priónicas, como la enfermedad de Creutzfeldt-Jakob, provienen de proteínas priónicas anormales. Las mutaciones genéticas y un proceso posttraduccional impulsan la neurodegeneración, que afecta tanto a los animales como a los humanos.

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