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Enfermedad de Castleman unicéntrica abdominal: una frenemia hepático-pancreático-biliar
Evangelia Florou1, Emeema Govindu1, Yoh Zen2
1Hepato-Pancreato-Biliary Surgery, King's College Hospital, London, GBR.
La enfermedad de Castleman unicéntrica (UCD) presenta desafíos de diagnóstico, a menudo imitando la malignidad. La resección quirúrgica es clave para el diagnóstico y el tratamiento, con seguimiento hematológico a largo plazo recomendado para todos los pacientes.
Área de la Ciencia:
- En el campo de la oncología
- Patología
- Gastroenterología quirúrgica
Sus antecedentes:
- La enfermedad de Castleman (CD) abarca trastornos linfoproliferativos raros, incluidas las formas unicéntricas (UCD) y multicéntricas (MCD).
- La UCD generalmente involucra un solo sitio y puede confundirse con una neoplasia maligna, lo que complica el diagnóstico y el tratamiento.
- La UCD abdominal se presenta como una masa solitaria, que a menudo requiere experiencia quirúrgica hepato-pancreático-biliar (HPB).
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