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Informe de caso: La brecha fantasma: un caso de ausencia congénita de pericardio revelado por imágenes avanzadas
Gou Junqi1, Yao Fengyou1, Liu Chaohui1
1Department of Cardiology, Geriatric Diseases Institute of Chengdu/Cancer Prevention and Treatment Institute of Chengdu, Chengdu Fifth People's Hospital (The Second Clinical Medical College, Affiliated Fifth People's Hospital of Chengdu University of Traditional Chinese Medicine), Chengdu, China.
La ausencia congénita del pericardio (CAP) es un defecto cardíaco raro. Este caso destaca su complejo diagnóstico, a menudo confundido con embolia pulmonar (EP), enfatizando la imagen avanzada para la identificación correcta.
Área de la Ciencia:
- Cardiología
- Embriología
- Radiología
Sus antecedentes:
- La ausencia congénita del pericardio (CAP) es una anomalía rara (prevalencia < 1:10,000), derivada de la atrofia cardinal común izquierda embrionaria.
- Los defectos pericárdicos son el resultado de la CAP, lo que puede conducir a una hernia cardíaca.
- El diagnóstico precoz es crucial para un tratamiento adecuado y para evitar diagnósticos erróneos.
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