Video Experimental Relacionado

Updated: Jul 2, 2026

Isometric and Eccentric Force Generation Assessment of Skeletal Muscles Isolated from Murine Models of Muscular Dystrophies
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Isometric and Eccentric Force Generation Assessment of Skeletal Muscles Isolated from Murine Models of Muscular Dystrophies

Published on: January 31, 2013

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Hiperactividad, comportamientos compulsivos y flexibilidad alterada en modelos de ratón de distrofia muscular de

Faouzi Zarrouki1, Léa Ceschi1, Rubén Miranda2

  • 1Université Paris-Saclay, CNRS, Institut des Neurosciences Paris-Saclay, Campus CEA Saclay, 151 route de la Rotonde, 91400 Saclay, France.

Neurobiology of disease
|January 11, 2026
PubMed
Resumen

Los modelos de ratón de distrofia muscular de Duchenne muestran hiperactividad e inflexibilidad, vinculados a deficiencias específicas de la distrofina cerebral. Estos hallazgos ofrecen información sobre las comorbilidades del trastorno por déficit de atención/hiperactividad en pacientes con DMD.

Palabras clave:
Distrofinas cerebralesComorbilidades relacionadas con el cerebroDistrofia muscular de DuchenneFunciones ejecutivasComportamiento en el hogarSistema IntellicageTrastorno del neurodesarrollo

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