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Inmunoterapias en la encefalitis autoinmune

Cynthia M C Lemmens1, Agnes Van Sonderen1, Maarten J Titulaer2

  • 1Department of Neurology, Haaglanden Medical Center, The Hague, South Holland, The Netherlands.

Handbook of clinical neurology
|January 12, 2026
PubMed
Resumen

La encefalitis autoinmune (EA) es un trastorno cerebral inflamatorio causado por autoanticuerpos. La inmunoterapia temprana, incluidos los esteroides y la IVIg, puede conducir a la remisión y mejorar los resultados.

Palabras clave:
AutoanticuerposEncefalitis autoinmune (EA)GAD65InmunoterapiaLGI1NMDARRefractario

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Área de la Ciencia:

  • Neuroinmunología
  • Neurología
  • Medicina Interna

Sus antecedentes:

  • La encefalitis autoinmune (EA) es una afección neurológica inflamatoria diversa.
  • Surge de autoanticuerpos dirigidos contra componentes neuronales, lo que provoca síntomas variados como deterioro cognitivo, convulsiones y disfunción autonómica.

Objetivo del estudio:

  • Resumir la comprensión actual de la encefalitis autoinmune.
  • Esbozar las estrategias diagnósticas y terapéuticas para la EA.

Principales métodos:

  • Revisión de la literatura existente sobre encefalitis autoinmune.
  • Análisis de las presentaciones clínicas, los enfoques diagnósticos y los resultados del tratamiento.

Principales resultados:

  • La EA se presenta de forma heterogénea según el autoantígeno específico.
  • El diagnóstico temprano y la inmunoterapia son cruciales para un pronóstico favorable.
  • Los tratamientos de primera línea incluyen glucocorticoides en dosis altas, IVIg y plasmaféresis.
  • Las terapias de segunda línea como el rituximab o la ciclofosfamida se utilizan para casos graves o recurrentes.

Conclusiones:

  • La encefalitis autoinmune requiere un diagnóstico oportuno y una inmunoterapia agresiva.
  • Aunque existen tratamientos establecidos, se necesita más investigación, incluidos ensayos controlados aleatorios.
  • Están surgiendo nuevas terapias, pero su eficacia requiere más datos.