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Síndrome de no compresión del ventrículo izquierdo

Kateryna Strubchevska1, Olena Strubchevska2, Marko Kozyk3

  • 1From the Departments of Medicine, New York Medical College and Westchester Medical Center, Valhalla, NY.

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|February 13, 2026
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Resumen

La no compresión del ventrículo izquierdo (LVNC) es una desafiante enfermedad del músculo cardíaco con clasificaciones debatidas y una compleja base genética. Sus criterios de diagnóstico se superponen con otras afecciones, lo que complica la identificación precisa y la evaluación de riesgos.

Palabras clave:
RMCmiocardiopatíaecocardiografíagenéticainsuficiencia cardíacano compresión del ventrículo izquierdo

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Área de la Ciencia:

  • Cardiología
  • Genética
  • Diagnóstico Médico

Sus antecedentes:

  • La no compresión del ventrículo izquierdo (LVNC) es una miocardiopatía primaria que afecta al ventrículo izquierdo, con posible afectación del ventrículo derecho o biventricular.
  • Puede coexistir con trastornos neuromusculares, defectos cardíacos congénitos y anomalías cromosómicas.
  • Las clasificaciones actuales son objeto de debate, con diferentes puntos de vista de las principales sociedades cardiovasculares sobre su estado genético o no clasificado.

Objetivo del estudio:

  • Explorar los desafíos de clasificación y los criterios de diagnóstico de la no compresión del ventrículo izquierdo (LVNC).
  • Discutir el panorama genético y la superposición fenotípica de la LVNC con otras miocardiopatías.
  • Destacar las implicaciones de los criterios de diagnóstico en diversos estados fisiológicos.

Principales métodos:

  • Revisión de la literatura existente y los sistemas de clasificación de la LVNC.
  • Análisis de los criterios de diagnóstico basados en la relación miocardio trabeculado/miocardio compactado.
  • Examen de la superposición fenotípica con las miocardiopatías hipertrófica y dilatada.

Principales resultados:

  • La clasificación de la LVNC sigue siendo controvertida debido a su heterogeneidad y a las diferentes categorizaciones de las sociedades.
  • Los criterios de diagnóstico de la LVNC se encuentran en personas sin miocardiopatía, incluidos atletas y mujeres embarazadas.
  • La base genética de la LVNC es compleja, con una superposición significativa con otras miocardiopatías.

Conclusiones:

  • La clasificación tradicional de la LVNC se ve desafiada por su compleja genética y sus ambigüedades diagnósticas.
  • El diagnóstico preciso de la LVNC requiere una cuidadosa consideración de su naturaleza heterogénea y la posible superposición con otras afecciones.
  • A pesar de ser a menudo asintomática, la LVNC conlleva riesgos que incluyen eventos tromboembólicos, disfunción cardíaca, arritmias y muerte súbita cardíaca.