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Published on: January 17, 2011
Ventilación asistida para pacientes con fibrosis quística
JAMA
|May 5, 1978
Resumen
La ventilación mecánica ofrece bajas tasas de supervivencia para los pacientes con fibrosis quística (FC), y la mayoría muere durante o poco después del tratamiento. Considere la ventilación solo para pacientes con FQ con insuficiencia respiratoria aguda y buen estado basal.
Área de la Ciencia:
- Pulmonología Pulmonología.
- Medicina de cuidados críticos Medicina de cuidados críticos.
- La pediatría es la medicina de los niños.
Sus antecedentes:
- La fibrosis quística (FQ) es un trastorno genético que afecta a los pulmones.
- La ventilación asistida es una intervención de cuidados críticos para la insuficiencia respiratoria.
Objetivo del estudio:
- Evaluar los resultados de la ventilación asistida en pacientes con fibrosis quística.
- Para determinar las tasas de supervivencia y el pronóstico a largo plazo para los pacientes con FQ que reciben ventilación mecánica.
Principales métodos:
- Análisis retrospectivo de 46 pacientes con fibrosis quística (de 1 mes a 32 años) sometidos a 51 episodios de ventilación asistida.
- Recopilación de datos sobre la mortalidad durante la ventilación, después de la interrupción y la supervivencia a largo plazo.
Principales resultados:
- Alta tasa de mortalidad: el 69% murió durante la ventilación mecánica, y el 12% murió después de la terapia.
- Supervivencia a largo plazo limitada: solo 3 pacientes sobrevivieron más de un año después del alta.
- Los resultados son más pobres en comparación con otras causas de la enfermedad pulmonar obstructiva crónica (EPOC).
Conclusiones:
- La ventilación mecánica se asocia con malos resultados en pacientes con fibrosis quística.
- Los pacientes con FQ avanzada que no responden al tratamiento óptimo no son candidatos ideales.
- Se puede considerar la ventilación para seleccionar pacientes con FQ con insuficiencia respiratoria aguda y buen estado basal.
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