:

D G Wilson1, M F Bellamy, M W Ramsey

  • 1Congenital Heart Disease Center, University Hospital of Wales Healthcare NHS Trust, Heath Park, Cardiff, Wales, UK.

Circulation
|February 23, 1999
PubMed
まとめ

マーファン症候群は,内皮細胞におけるフィブリリンの機能であるフロー媒介の膨張を損なうが,アゴニスト媒介の膨張を保持する. これは,フィブリリンが,内皮のメカニカル伝導と酸化窒素の放出の鍵であることを示唆しています.

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